Gref tus tsos mob

Gref tus tsos mob
Gref tus tsos mob

Video: Gref tus tsos mob

Video: Gref tus tsos mob
Video: Tshuaj theem vim li cas thiaj tau nqi ?/ Siv kho mob dab tsi?/paris polyphylla use for? 2024, Lub rau hli ntuj
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Graefe's Syndrome (Grefe-Usher's Syndrome) yog pigmented dystrophy, ua ke nrog kev hnov lus ntawm qhov sib txawv ntawm qhov hnyav, mus txog rau qhov lag ntseg. Lub npe ntawm cov tsos mob tau piav qhia los ntawm qhov tseeb tias Grefe tau piav qhia thawj zaug, thiab tom qab ntawd Usher. Yog li ob lub npe ntawm tus kab mob.

Tus kab mob tuaj yeem tau txais los ntawm kev rov ua dua tshiab (frequency 43.5%).

Graefe cov tsos mob
Graefe cov tsos mob

Tus kab mob no tau nthuav tawm hauv qhov maj mam nce ophthalmoplegia, uas, nce zuj zus, tuaj yeem ua rau lub qhov muag tsis pom kev thiab tag nrho ptosis. Hauv yuav luag ib nrab ntawm cov neeg mob, kom meej meej, hauv plaub caug feem pua, cov tsos mob tau ua ke nrog pigmentary dystrophy. Nws tseem yuav tsum tau hais txog kev hloov pauv loj heev cuam tshuam rau hauv nruab nrab paj hlwb.

Grefe cov tsos mob yog ib yam kab mob uas feem ntau cuam tshuam rau cov me nyuam yug los tsis yog los ntawm txoj kev, tab sis los ntawm kev phais. Tus kab mob no tseem hu ua "Setting Sun Syndrome". Vim li cas nws thiaj muaj lub npe zoo li no? Qhov no yog vim qhov tshwm sim ntawm tus neeg mob: tus menyuam txo qis nws ob lub qhov muag, thiab daim tawv muag sab sauv ntawm lub sijhawm no pib exfoliate.

Dab tsi ua rau tus kab mob no tsis kaj siab?

Graefe's symptom photo
Graefe's symptom photo

Nws yuav tsum tau muab sau tseg tias yog cov tsos mob tshwm sim ntawm qhovlub sij hawm thaum tus me nyuam hloov txoj hauj lwm, uas yog, muaj lub caij nyoog uas tus kab mob yuav ploj mus ntawm nws tus kheej tom qab ib pliag. Yog tias qhov no tshwm sim tas li, koj yuav tsum tau mus ntsib kws kho mob sai. Qhov no tuaj yeem piav qhia los ntawm qhov tseeb tias thawj kis yog tshwm sim los ntawm qhov tsis paub qab hau ntawm lub paj hlwb, thiab qhov thib ob los ntawm kev nce hauv intracranial siab.

Yog tias koj dheev pom cov tsos mob ntawm tus kab mob no, nws yog qhov zoo dua los tiv tauj tsis yog ib tus kws tshaj lij, tab sis ob peb zaug ib zaug, txhawm rau piav qhia cov duab tiav. Koj yuav tsum mus ntsib kws kho mob hlwb.

Hnov txog tus kab mob no los ntawm tus kws kho mob, koj yuav tsum tsis txhob tso tseg rau tus menyuam. Nws kuj tsis tsim nyog hla qhov kev kuaj mob "los ntawm pob ntseg", vim tias Graefe cov tsos mob yuav tsum tau kho, zoo li lwm yam kab mob. Kev kuaj pom tus kab mob sai dua, qhov zoo dua, vim tias nyob rau theem ua ntej, kev kho mob me me tuaj yeem faib nrog. Tab sis yog tias koj ncua sijhawm, koj yuav xav tau chav kawm hnyav.

Qee lub sij hawm tus kab mob no mus nws tus kheej. Nrog lub hnub nyoog, lub paj hlwb thaum kawg matures, thiab cov syndrome ploj. Txawm li cas los xij, koj yuav tsum sab laj nrog tus kws kho mob tshwj xeeb uas yuav sau tag nrho cov kev ntsuam xyuas tsim nyog, suav nrog ultrasound ntawm lub hlwb. Tsuas yog tom qab dhau qhov kev ntsuam xyuas nws thiaj li tuaj yeem txiav txim siab txog qhov xwm txheej ntawm cov txheej txheem tsis tu ncua thiab txiav txim siab qhov kev kuaj mob thiab kev kho mob, yog tias tsim nyog.

Nws yog ib qho tseem ceeb uas yuav tsum nco ntsoov tias tsis muaj qhov xwm txheej twg koj yuav tsum cuam tshuam cov kev kho mob uas koj tus kws kho mob tau sau tseg yog tias koj pom qhov tshwm sim me ntsis. Qhov no tsuas yog qhov pib xwb, tsis yog qhov kawg nkaus xwb, yuav tsum coj txhua yam mus rau qhov kawg.

Tus kws tshaj lij yuav txiav txim siab seb tus neeg mob yuav tsum ua li caschav kho mob - tom tsev lossis hauv tsev kho mob. Intracranial siab yog ib qho teeb meem loj heev, tab sis nco ntsoov tias Graefe cov tsos mob yog qhov lees paub ntawm nws qhov muaj nyob.

Gref tus tsos mob, duab:

Graefe's Syndrome
Graefe's Syndrome

Koj tus menyuam yog yam khoom muaj nqis tshaj plaws uas koj muaj, yog li ceev faj. Tau kawg, koj yuav tsum tsis txhob ntshai vim tsis muaj laj thawj, tab sis yog tias tsis ntseeg, sab laj nrog kws kho mob hlwb.

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