Charcot's Syndrome. Yuav ua li cas nrog Charcot tus kab mob?

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Charcot's Syndrome. Yuav ua li cas nrog Charcot tus kab mob?
Charcot's Syndrome. Yuav ua li cas nrog Charcot tus kab mob?

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Charcot's syndrome - nws yog dab tsi thiab nws tshwm sim li cas? Nws yog rau cov lus nug no uas peb yuav mob siab rau kab lus no.

charcot syndrome
charcot syndrome

Kev piav qhia tus kab mob

Charcot's syndrome (los yog tsis sib haum xeeb claudication) yog ib yam kab mob uas tshwm sim los ntawm qhov tshwm sim, nrog rau qhov mob thiab tsis muaj zog nyob rau hauv qis qis thaum taug kev. Xws li kev tshwm sim feem ntau ua rau tus neeg mob nres, vim tias thaum so cov tsos mob muaj npe xyaum tsis thab. Feem ntau, tib neeg ntsib qhov kev sib txawv no los ntawm:

  • kev quav dej quav cawv thiab haus luam yeeb ntau dhau;
  • overweight;
  • ntshav siab;

Cov tsos mob tseem ceeb

Charcot's syndrome yog ib qho mob hnyav uas ua rau tus neeg mob tsis xis nyob thiab ua rau nws lub neej tsis zoo. Nrog xws li kev sib txawv, ib tug neeg feem ntau yws yws ntawm kev qaug zog, nrog rau qhov tsis xis nyob thiab mob nyob rau hauv qis extremities thaum taug kev, tshwj xeeb tshaj yog nyob rau hauv cheeb tsam gluteal thiab calf nqaij. Tseem muaj cov xwm txheej thaum qhov mob nyob hauv cov leeg nqaij ntawm tus ncej puab thiab sab nraub qaum. Raws li cov neeg mob kuaj mob Charcot, tus kab mob ib nrab txo qis thiab tsis muaj zog tam sim ntawdso luv.

Kab mob Charcot
Kab mob Charcot

Nrog rau cov kab mob zoo li no nyob rau hauv qhov chaw ntawm qhov qis qis, tus neeg mob feem ntau muaj trophic thiab vegetative-vascular ntshawv siab (piv txwv li, acrocyanosis, txias ntawm ko taw, marbling ntawm daim tawv nqaij thiab lawv cov kev hloov dystrophic, tsis muaj. mem tes ntawm cov hlab ntsha ntawm ob txhais taw, nrog rau gangrene ntawm cov ntiv tes, uas feem ntau txuas mus ze).

Ntawm lwm yam, Charcot's syndrome kuj yog tus cwj pwm los ntawm degenerative-dystrophic hloov hauv cov pob txha thiab pob qij txha (hypertrophy ntawm tus kheej ntu, pob txha mos degeneration, pob txha sequesters, osteophytes, intra-articular thiab spontaneous fractures ntawm tubular pob txha). Tsis tas li ntawd, looseness thiab txo rhiab heev ntawm cov pob qij txha ua rau muaj kev pheej hmoo ntawm kev raug mob.

Kev tshwm sim

Charcot's syndrome yog ib yam kab mob uas tshwm sim los ntawm kev puas tsuaj rau cov hlab ntsha ntawm ob txhais ceg (thrombangiitis, obliterating atherosclerosis, peripheral daim ntawv ntawm nonspecific aortoarteritis, thiab lwm yam). Kev mob ntawm tus neeg mob tshwm sim vim cov ntshav tsis txaus mus rau cov leeg nqaij ntawm sab qis. Tsis tas li ntawd, tus kab mob tuaj yeem tshwm sim los ntawm kev compression ntawm cauda equina hauv tus txha caj qaum, tsawg dua vim yog tus txha caj qaum ischemia hauv arteriovenous malformation lossis atherosclerosis ntawm aorta.

Charcot Marie Syndrome
Charcot Marie Syndrome

Kev kho mob

Kev kho rau kev sib cuam tshuam claudication yog kev kho ncaj qha ntawm tus kab mob tseem ceeb, uas yog cov hlab ntsha. Raws li txoj cai, nyob rau hauv cov xwm txheej zoo li no, kws kho mobqhia lawv cov neeg mob kom tso tseg txhua yam kev phem, txo qhov hnyav thiab ua raws li kev noj zaub mov nruj. Cov neeg mob kuj tau sau ib qho tshwj xeeb ntawm kev tawm dag zog lub cev uas yuav pab kov yeej cov tsos mob ntawm tus kab mob.

Raws li txoj kev kho kom zoo, lawv suav nrog kev noj ntau yam tshuaj. Lawv qhov kev txiav txim muab cov nyhuv analgesic thiab vasodilating. Cov khoom lag luam kuj tseem pab txo cov roj cholesterol thiab ua kom nyias nyias.

Thaum xav tau ceev, kev phais yog siv, thaum lub lumen ntawm cov hlab ntsha nthuav dav los ntawm kev ntxig ib lub catheter tshwj xeeb rau hauv nws.

Charcot-Marie-Tooth Syndrome

Qhov kev sib txawv no yog ib pawg ntawm cov kab mob ntawm cov kab mob tshwm sim los ntawm degeneration ntawm peripheral paj fibers. Nws yuav tsum raug sau tseg tshwj xeeb tshaj yog tias qhov sib txawv ntawm lub npe hu ua syndrome tuaj yeem ua raws li qhov sib txawv ntawm cov caj ces. Feem ntau ntawm cov kab mob no tau txais los ntawm autosomal dominant yam. Txawm li cas los xij, qhov sib txawv ntawm cov kab mob cuam tshuam nrog kev sib txuas ntawm X chromosome tau raug txheeb xyuas tam sim no.

Nrog rau qhov kev kuaj mob xws li Charcot-Marie syndrome, tus neeg mob tus txha caj qaum thiab cov hlab ntsha peripheral raug cuam tshuam. Axonal neuropathy lossis demyelinating neuropathy tuaj yeem txhim kho nyob ntawm qhov tshwj xeeb genetic defect.

Feem ntau nthuav tawm qhov sib txawv pib pib thaum hluas lossis hluas. Cov tsos mob ntawm cov pab pawg neeg ntawm tus kab mob no nce zuj zus mus, thiab cov kab mob loj zuj zus tuaj, ua rau muaj kev mob siab.kev tsis taus tuag.

Symptoms of deviation

Tus kab mob no pib tshwm sim nws tus kheej nrog atrophy ntawm cov leeg nqaij ntawm ob txhais ceg thiab tsis muaj zog. Sij hawm dhau mus, ob txhais taw ua deformed, thiab cov ntiv tes ua rauj-zoo li tus thiab loj. Cov menyuam yaus uas muaj qhov kev kuaj mob no yuav luag ib txwm muaj qhov qeeb ntawm kev loj hlob ntawm lub cev.

Charcot Marie Tut Syndrome
Charcot Marie Tut Syndrome

Kev kho mob ntawm caj ces

Tsis muaj kev kho tshwj xeeb rau tus mob pathological no. Txawm li cas los xij, txhawm rau txhim kho tus neeg mob txoj kev noj qab haus huv, cov kws kho mob feem ntau sau cov kev kho mob thiab kev ua haujlwm kho mob. Tsis tas li ntawd, cov neeg mob uas muaj qhov kev kuaj mob no nquag siv txhua yam khoom siv kho mob kom tshem tawm cov tsos mob ntawm qhov mob. Piv txwv li, nrog rau dai taw, ib qho orthopedic brace yog siv los ntxiv dag zog rau sab ceg, thiab lwm yam. Kev sab laj txog caj ces kuj tseem ceeb heev.

Von Willebrand tus kab mob

Nws yuav tsum tau sau tseg tshwj xeeb tias tsis yog Charcot's syndrome nkaus xwb yog cov kab mob sib kis. von Willebrand kab mob kuj kis tau los ntawm cov neeg hauv tsev neeg tam sim ntawd.

Raws li koj paub, qhov kev sib txawv ntawm qhov nthuav tawm yog hom kab mob tshwm sim feem ntau ua rau cov ntshav coagulation tsis zoo lossis cov txheej txheem coagulation. Txawm li cas los xij, feem ntau tus kab mob no kuj tshwm sim hauv lub neej vim yog kev ua ntawm lwm yam kab mob (uas yog, daim ntawv tau txais).

Charcot-willebrand Syndrome
Charcot-willebrand Syndrome

Cov tsos mob

Kev pheej hmoo los ntshav nrog qhov sib txawv no yog qhov tseem ceebtxawv nyob ntawm seb hom kab mob twg. Cov cim tseem ceeb ntawm qhov kev tsis sib haum xeeb no yog lub qhov ntswg ib ntus, qhov tsis zoo ntawm hematomas thiab bruises, los ntshav cov pos hniav, thiab lwm yam. Cov poj niam yuav muaj lub caij hnyav, thiab muaj feem yuav poob ntshav ntau thaum yug menyuam.

Kev kho mob

Cov neeg mob nrog qhov kev kuaj mob no tsis tas yuav muaj kev kho mob, tab sis lawv ib txwm muaj kev pheej hmoo los ntshav hnyav. Yog li, tus neeg mob yuav raug pom zoo siv tshuaj uas txo cov tsos mob ntawm tus kab mob no. Yog tias tus neeg mob tau teem sijhawm mus rau kev phais mob, ces cov kws kho mob yuav ua tiav kev tiv thaiv kev kho mob.

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