Pituitary qog: cov tsos mob, kev kho mob thiab qhov tshwm sim

Cov txheej txheem:

Pituitary qog: cov tsos mob, kev kho mob thiab qhov tshwm sim
Pituitary qog: cov tsos mob, kev kho mob thiab qhov tshwm sim

Video: Pituitary qog: cov tsos mob, kev kho mob thiab qhov tshwm sim

Video: Pituitary qog: cov tsos mob, kev kho mob thiab qhov tshwm sim
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Anonim

Lub hlwb yog tib neeg lub cev. Hauv nws qhov qis, ncaj qha rau hauv pob txha hnab tshos, yog lub caj pas pituitary. Cov tom kawg yog lub qog endocrine. Hais txog lub endocrine system. Lub caj pas pituitary yog lub luag haujlwm tsim cov tshuaj hormones uas ua haujlwm tseem ceeb. Qee tus ntawm lawv yog lub luag haujlwm rau kev loj hlob, lwm tus rau kev muaj peev xwm yug me nyuam, thiab lwm tus tswj cov metabolism. Qhov no yog qhov tshwm sim ntawm tus neeg noj qab haus huv. Tab sis cov txheej txheem no tuaj yeem ua tsis tiav. Cov kab mob zoo li no ua rau tsis muaj kev tswj hwm kev loj hlob ntawm cov hlwb uas hloov mus rau hauv cov qog. Feem ntau, cov formations no yog benign thiab, nrog rau kev kho kom raug, tsis ua rau muaj kev hem thawj rau lub neej. Txawm li cas los xij, tsis tshua muaj, tab sis tseem muaj cov qog nqaij hlav malignant. Tib neeg hu lawv cov qog nqaij hlav pituitary. Lawv tuaj yeem ua rau qee qhov tshwm sim loj heev. Yog li ntawd, tsis muaj teeb meem koj yuav tsum ncua sijhawm mus ntsib kws kho mob. Nyob rau lub sijhawm ua tib zoo saib xyuas cov kev hloov hauv lub cev yuav pab kom paub txog koj tus kheej nrog cov tsos mob ntawm cov qog pituitary. Hauv kab lus no, lawv yuav piav qhia meej. Tsis tas li, tus nyeem ntawv yuav tuaj yeem paub txog lwm txoj hauv kevTxoj hauv kev los kho cov kab mob no.

Neurological nam

Raws li tau hais los saum no, cov qog nqaij hlav hauv lub hlwb yog tsim los ntawm kev tsim cov qog pituitary txawv txav. Lub neoplasm yog nyob rau sab nraub qaum lossis pem hauv ntej thiab cuam tshuam ncaj qha rau kev tsim cov tshuaj hormones. Lawv qhov sib npaug hauv lub cev cuam tshuam. Qhov no ua rau muaj teeb meem ntau yam paj hlwb.

Raws li kev txheeb cais, cov qog pituitary tau kuaj pom hauv cov txiv neej thiab poj niam uas muaj zaus tib yam. Nws tsis tuaj yeem sib cav tias ib tus ntawm lawv muaj kev cuam tshuam ntau dua rau cov kab mob no. Txawm li cas los xij, feem ntau cov neeg mob tuaj nrog pathologies thaum muaj hnub nyoog 30-40, yog li lawv tuaj yeem suav nrog hauv pawg pheej hmoo.

Cov meninges tuaj yeem ua rau muaj kev loj hlob ntawm cov qog. Lawv loj hlob mus rau hauv lub caj pas pituitary, ua rau muaj kev cuam tshuam tsis zoo rau nws. Qee qhov xwm txheej, nws tsis tuaj yeem kuaj pom pathology nyob rau theem pib, txij li nws tuaj yeem txhim kho asymptomatically. Tus neeg ntawd tsis xav tias muaj kev hloov pauv. Nrog rau cov duab kho mob zoo li no, qhov tsim tau raug kuaj pom los ntawm lub sijhawm thaum kuaj xyuas, vim tias tsis muaj cov cim qhia pom tseeb ntawm cov qog pituitary.

Cov kab mob no, raws li kev txheeb cais, yog 15% ntawm tag nrho cov kab mob intracranial. Qee hom mob qog noj ntshav teb zoo rau kev kho mob. Txawm li cas los xij, nws yog ib qho tseem ceeb kom nkag siab tias qhov txiaj ntsig zoo tsuas yog ua tau nrog kev kuaj mob raws sij hawm.

pituitary qog
pituitary qog

Kev faib tawm

Hauv tshuaj, lub paj hlwb pituitary qog tau muab faib ua ob hom:

  • malignant;
  • zoo.

Raws li tau hais los saum toj no, tom kawg yog ntau dua. Lawv hu ua adenomas. Cov qog nqaij hlav tsis tshua kuaj pom. Hloov cov hlwb ntawm ib qho benign tsim muaj peev xwm ua tau lub luag haujlwm ntawm cov neeg noj qab haus huv, txawm tias qee qhov. Cov qog nqaij hlav ntawm hom no nce qhov loj me me, yog li lawv tsis ua rau muaj kev puas tsuaj rau kev noj qab haus huv. Yog tias pom, lawv raug tshem tawm. Kev mob ntshav qab zib yog qhov tsawg heev.

Cov qog nqaij hlav tsis tsuas loj hlob, nyem cov ntaub so ntswg, tab sis kuj muaj peev xwm nkag mus rau lawv, uas yog qhov txaus ntshai heev. Cov kev xaiv kho mob rau cov kev loj hlob no yuav txawv nyob ntawm hom.

Cov tsos mob ntawm tus qog pituitary
Cov tsos mob ntawm tus qog pituitary

Yog vim li cas

Tam sim no, cov tshuaj tseem tsis tau paub meej txog qhov ua rau ua rau kev loj hlob ntawm cov qog pituitary. Cov kws tshawb fawb feem ntau xav hais tias kev yug me nyuam ua lub luag haujlwm tseem ceeb. Yog hais tias ib tug neeg hauv tsev neeg twb muaj tus kab mob no lawm, ces yuav tsum tau mus kuaj tsis tu ncua thiaj li yuav teb tau raws sijhawm.

Ntxiv rau qhov kev hloov pauv, cov kws kho mob txheeb xyuas ntau qhov laj thawj uas tuaj yeem ua rau pib ntawm kev loj hlob ntawm kev kawm. Cov no suav nrog:

  • mob hlwb;
  • ua txhaum ntawm kev ua haujlwm ntawm cov qog ua haujlwm ntawm cov kab mob endocrine;
  • kab mob sib kis ntawm lub paj hlwb;
  • kab mob caj ces;
  • siv sijhawm ntev ntawm cov tshuaj hormonal;
  • ntau ntawm cov tshuaj hormones hypothalamic;
  • yam tsis zoo cuam tshuam rau tus menyuam hauv plab.

Adenoma

Cov qog nolub caj pas pituitary, cov tsos mob uas yuav tau tham hauv qab no, yog benign. Feem ntau tshwm sim. Size varies:

  • kab ntawm 40 mm lossis ntau dua - loj adenomas;
  • ntau tshaj 10 hli - macroadenomas;
  • tsawg dua 10 hli - microadenomas;
  • tsis tshaj 3 hli - picoadenomas.

Cov ntaub ntawv kev kawm raug cais tsis yog los ntawm qhov loj, tab sis kuj yog los ntawm kev ua haujlwm. Raws li qhov kev ntsuas no, lawv paub qhov txawv:

  • hormonally inactive - cov hlwb puas tsis koom nrog kev sib txuas ntawm cov tshuaj hormones;
  • hormonally active - kev kawm tsim cov tshuaj hormones.
Cov cim qhia ntawm cov qog pituitary
Cov cim qhia ntawm cov qog pituitary

Hom tshuaj hormonally nquag adenomas

Cov kev tsim tawm uas tsim cov tshuaj hormones muab faib ua hom nyob ntawm cov khoom nquag. Cia wb mus saib lawv.

  • Prolactinomas yog cov qog uas tsim tawm ntau tshaj ntawm cov tshuaj hormone prolactin. Nws yog lub luag haujlwm rau kev zais ntawm cov qog mammary thiab ua haujlwm ntawm zes qe menyuam. Cov tsos mob hauv cov txiv neej uas muaj hom qog pituitary yog galactorrhea thiab gynecomastia. Thawj pathology manifests nws tus kheej nyob rau hauv daim ntawv ntawm secretions uas zoo ib yam li cov kua mis. Thiab gynecomastia yog kev loj hlob ntawm cov qog mammary hauv cov txiv neej. Cov poj niam pom cov tsos mob zoo sib xws. Lub hauv siab ua mob, nce qhov loj. Mis ntau lawm pib. Muaj cov kev xav zoo ib yam li thaum cev xeeb tub. Ntxiv nrog rau cov cim qhia no, hauv cov poj niam, kev coj khaub ncaws mus yuam kev. Amenorrhea tuaj yeem tsim, ua rau muaj menyuam tsis taus.
  • Corticotropinomas - tsim tawm uas tsim tawm ntau dhaucorticosteroid cov tshuaj hormones. Hauv qhov ntau, lawv tuaj yeem ua rau Cushing tus kab mob. Ua haujlwm ntawm cov qog adrenal. Cov neeg mob uas muaj cov qog no qhia cov tsos mob hauv qab no: kev puas siab puas ntsws, kev hloov ntawm lub ntsej muag, bruises, hnub nyoog me ntsis thiab stretch marks tshwm rau ntawm daim tawv nqaij, plaub hau loj hlob ntau dhau.
  • Somatotropinomas. Hom kev tsim no synthesizes kev loj hlob hormone - somatotropin. Cov tsos mob nyob rau hauv cov txiv neej nrog lub qog pituitary ntawm hom no yog ib qho kev nce hauv qhov loj ntawm ko taw, thickening ntawm cov pob txha. Cov cim no tuaj yeem tshwm sim hauv cov poj niam thiab menyuam yaus. Nyob rau hauv ib tug me nyuam, pathology ua rau gigantism, uas yog tshwm sim los ntawm kev loj hlob ntau dhau.
  • YThyrotropinomas. Kev kawm txhawb kev tsim cov thyroid-stimulating hormone. Nws yog ib qho tseem ceeb rau kev ua haujlwm ntawm cov thyroid caj pas. Nyob rau hauv ntau qhov, nws provokes kev loj hlob ntawm hypothyroidism thiab thyrotoxicosis. Raws li rau tom kawg pathology, cov tsos mob hauv qab no tau pom nrog nws: poob phaus, tsis qab los noj mov, pw tsaug zog, tawv nqaij qhuav, mob paj hlwb. Cov tsos mob ntawm hypothyroidism yog txawv me ntsis. Cov kab mob no tau tshwm sim los ntawm cov dej noo ntau dhau ntawm daim tawv nqaij, khov ntawm cov extremities, txo qis lub peev xwm, thiab qeeb qeeb.
  • Gonadotropinomas - ntau dhau ntawm cov tshuaj gonadotropic, uas yog lub luag haujlwm rau kev sib deev. Cov tsos mob ntawm cov poj niam uas muaj cov qog pituitary ntawm hom no: kev ua txhaum ntawm lub voj voog lossis ua tiav kev coj khaub ncaws, los ntshav hauv tsev menyuam. Cov txiv neej feem ntau yuav tsim impotence, gynecomastia.
hlwb pituitary qog
hlwb pituitary qog

malignant qog

Txawm li cas los xij, tsis zoo li cov kab mob phem, cov kab mob phem ua rau muaj kev hem thawj rau tib neeg. Deformed hlwb plam tag nrho cov khoom muaj nyob rau hauv cov neeg noj qab nyob zoo. Lawm, lawv tsis muaj peev xwm txawm tias ib feem ua lawv txoj haujlwm. Vim qhov kev hloov pauv no, cov hlwb pib loj hlob uncontrollably. Kev kawm nkag mus rau hauv lymphatic thiab cov hlab ntsha, nrog rau cov ntaub so ntswg nyob ze. Kev loj hlob sai heev, nquag mus rau metastasis.

Feem ntau, txawm tias tom qab kho tau zoo, muaj qhov rov ua dua tshiab. Txawm li cas los xij, nws yuav tsum tau muab sau tseg tias cov qog malignant yog qhov nyuaj heev los kho. Ib qho kev pom zoo rau kev kho mob phais yog ua tau tsuas yog nyob rau theem pib, kom txog rau thaum cov tsim pib loj hlob mus rau cov ntaub so ntswg nyob sib ze. Yog tias qhov no tau tshwm sim thiab muaj qhov txhab nrog metastases, cov qog ua haujlwm tsis tau.

Kev loj hlob ntawm cov qog pituitary
Kev loj hlob ntawm cov qog pituitary

Pituitary qog: cov tsos mob ntawm cov poj niam thiab txiv neej

Cov tsos mob sib txawv qhia tias muaj qog nqaij hlav. Feem ntau ntawm lawv yog cov tsis kaj siab heev thiab tsis tso cai rau ib tug neeg kom tag nrho lub neej. Saum toj no, me ntsis twb tau hais txog cov cim qhia uas tshwm sim adenomas ntawm ntau hom. Txawm li cas los xij, nws yog ib qho tsim nyog los qhia txog qhov feem ntau ntawm lawv. Lub insidiousness ntawm tus kab mob no nyob rau hauv lub fact tias tej zaum cov pathology yog asymptomatic - nyob rau hauv li 20% ntawm cov neeg mob. Nrog rau cov kab mob zoo li no, nws yog qhov teeb meem zoo los kuaj xyuas nws. Hauv lwm qhov xwm txheej, cov tsos mob tau hais. Yog li, dab tsi qhia tias muaj qog nqaij hlav:

  • plaub hau poob hnyav;
  • txo qiskev pom;
  • cov ntxhais muaj lub cev tsis sib xws;
  • qhov tseem ceeb nce ntawm ko taw thiab txhais tes;
  • txiv neej qhia poj niam deev yam ntxwv;
  • mob hnoos qeev;
  • nrawm nrawm / poob;
  • drowsiness, qaug zog, txo kev ua haujlwm, mob taub hau, pom ob lub qhov muag;
  • paj hlwb, tics, convulsions, dementia, fainting;
  • overeating;
  • puffiness, lub ntsej muag hloov pauv (cov hniav txav sib nrug, qhov ntswg loj, hloov tom).

Cov tsos mob no tsis yog tshwj xeeb. Ib txhia ntawm lawv tshwm sim nyob rau hauv lwm yam kab mob. Txawm li cas los xij, lawv yuav tsum tsis txhob raug ignored, vim cov qog pituitary tuaj yeem loj hlob sai, thiab qhov no, raws li, yuav ua rau muaj qhov tshwm sim loj.

Kev kuaj mob dav dav

Qee zaum, cov tsos mob ntawm tus kab mob no, raws li lawv hais, pom tseeb. Piv txwv li, tus kws kho mob tuaj yeem kuaj xyuas tsuas yog hauv kev tshuaj ntsuam xyuas yam tsis muaj kev tshuaj xyuas ntxiv yog tias qee qhov ntawm lub cev loj tuaj (acromegaly). Itsenko-Cushing tus kab mob kuj qhia tau hais tias muaj ib tug neoplasm. Cov neeg raug kev txom nyem los ntawm nws yog qhov txawv ntawm cov yam ntxwv ntawm kev hloov pauv hauv qhov tsos. Tsis tas li ntawd, kev kuaj mob ntawm cov qog pituitary yog ua raws li cov cim qhia sab nraud hauv cov menyuam yaus uas muaj kev cuam tshuam loj heev.

Yog tias tus kws kho mob xav tias muaj kev kawm, tus neeg mob tau teem sijhawm mus kuaj. Nws suav nrog:

  • xam tomography, radiography (zoo thaum muaj qog loj), MRI thiab angiography;
  • tshuaj ntsuam tshuaj hormone - kuaj ntshav thiab zis;
  • tshuaj ntsuam qhov muag pom kev;
  • cerebrospinal kua biopsy.

Kev kuaj mob zoo tshaj plaws yog tomography. Txoj kev tshawb no tso cai rau koj los txiav txim siab qhov chaw ntawm cov qog thiab nws qhov loj me.

kho mob qog pituitary

Vim tias qhov tsim no muaj ntau hom, kev kho mob raug xaiv nyob ntawm lawv. Tsis tas li ntawd, thaum xaiv ib qho kev kho mob, tus kws kho mob tau saib xyuas rau theem ntawm tus kab mob, nrog rau qhov loj ntawm cov qog. Raws li kev sib xyaw ua ke ntawm cov xwm txheej no, kev phais, kev kho mob lossis kev kho hluav taws xob tau raug sau tseg. Qee zaum, kev kho mob nyuaj yog siv.

Nws yog ib qho tseem ceeb uas yuav tsum nco ntsoov tias nrog qog nqaij hlav, tsis muaj teeb meem koj yuav tsum vam khom koj tus kheej lub zog. Kev kuaj mob thiab kev kho mob yuav tsum tau ua los ntawm tus kws kho mob uas tsim nyog nkaus xwb. Qhov kev txiav txim zaum kawg yog ua nyob rau hauv pawg sab laj, qhov twg neurosurgeons, endocrinologists thiab neurologists yeej ib txwm muaj.

Kev tshem tawm cov qog pituitary
Kev tshem tawm cov qog pituitary

Tshuaj kho mob

Kev kho tshuaj tsuas yog siv yog tias cov qog pituitary yog qhov zoo. Ua ntej xaiv cov tshuaj, tus nqi ntawm nws txoj kev loj hlob thiab kev koom tes hauv kev tsim cov tshuaj hormones yog txiav txim siab. Yog tias, raws li cov txheej txheem kawg, cov kab mob tsis ua haujlwm, cov tshuaj dopamine agonists, xws li Cabergoline lossis Bromocriptine, raug tshuaj. Cov tshuaj no muaj peev xwm tswj kev tsim cov tshuaj hormones, txo cov qog loj. Kuj tseem muaj cov xwm txheej zoo li no uas qhov tsim tau ploj mus yam tsis muaj kev cuam tshuam kev phais.

Tshuaj raug xaiv nyob ntawm hom tshuaj hormones, uas nyob rau hauv lub cevtshaj. Piv txwv li, Sandostatin thiab Pegvisomant thaiv qhov kev txiav txim ntawm kev loj hlob hormone, thaum Cyproheptadine txo cov corticosteroids.

Kev kho hluav taws xob

Yog tias kev kho mob phais yog contraindicated rau qee qhov laj thawj, cov neeg mob tau txais kev kho hluav taws xob. Txoj kev no muaj nyob rau hauv irradiating lub qog. Tus kws kho mob xaiv cov koob tshuaj raws li qhov loj ntawm qhov tsim thiab nws hom. Cov txiaj ntsig zoo tsis tuaj sai. Qee zaum kev kho mob yuav kav ntev li ob peb xyoos. Nws qhov zoo dua yog tias cov qog yog irradiated los ntawm txhua sab, vim nws txo qhov loj me. Thaum cov txheej txheem, tus neeg mob tus mob yog saib xyuas los ntawm tus kws kho mob tuaj koom. Kev suav tomography tau ua tas li kom pom tias neoplasm teb li cas rau kev kho.

Nws yog ib qho tseem ceeb kom paub tias hluav taws xob muaj ntau yam kev phiv. Nws kuj siv tsis tau yog tias cov qog nyob ze ze ntawm cov hlab ntsha ntawm qhov muag.

Surgery

Kev tshem tawm cov qog pituitary yog kev kho mob zoo tshaj plaws. Ua ntej npaj txoj haujlwm, tus kws kho mob txiav txim siab qhov chaw thiab qhov loj ntawm neoplasm. Raws li txoj cai, nws raug tshem tawm los ntawm cov pob txha sphenoid cranial los yog frontally, siv cov khoom siv kho qhov muag tshwj xeeb.

Tam sim no, feem ntau cov kws phais neeg nyiam siv endoscopic transsphenoidal phais kom tshem tawm cov qog. Nws yog nqa tawm los ntawm qhov ntswg qhov ntswg. Hom kev cuam tshuam no muaj kev nyab xeeb raws li qhov ua tau, vim nws tsis tas yuav muaj kev phais. Thiab qhov no txo qhov kev pheej hmoo ntawm kev tsim ntau yam teeb meem. Kev ua haujlwm los ntawm qhov ntswg nkag yog ua nrogendoscopic sojntsuam thiab cov cuab yeej tshwj xeeb.

Ntau zaus, tom qab kev phais, cov neeg mob tau muab tshuaj thiab kho hluav taws xob.

Endoscopic transsphenoidal phais
Endoscopic transsphenoidal phais

Huab cua

Nrog cov qog pituitary, qhov kev cia siab nyob ntawm ntau yam. Lub sijhawm kuaj mob, kev ua haujlwm hormonal thiab qhov loj ntawm kev tsim yog qhov tseem ceeb heev. Somatotropinoma thiab prolactinoma yog qhov nyuaj rau kho. Tsuas yog 25% ntawm cov neeg mob tau kho tag nrho. Qhov kev pheej hmoo ntawm kev rov ua tiav hauv cov neeg mob nrog lwm hom adenomas yog siab - 80%. Nws yog qhov ua tau kom ua tiav cov kev ua haujlwm ntawm cov hlab ntsha ntawm optic tsuas yog tias tus kab mob tau kuaj pom thaum pib ntawm txoj kev loj hlob. Hauv cov theem tom qab, cov txheej txheem pathological twb tsis rov qab los.

Pom zoo: