Mastocytosis hauv menyuam yaus: ua rau, kho thiab qhov tshwm sim

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Mastocytosis hauv menyuam yaus: ua rau, kho thiab qhov tshwm sim
Mastocytosis hauv menyuam yaus: ua rau, kho thiab qhov tshwm sim

Video: Mastocytosis hauv menyuam yaus: ua rau, kho thiab qhov tshwm sim

Video: Mastocytosis hauv menyuam yaus: ua rau, kho thiab qhov tshwm sim
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Anonim

Me nyuam yaus muaj mob thiab tsis muaj leej twg yuav dim ntawm nws. Nws yog qhov zoo yog tias tus mob kis tau sai, tab sis nws kuj tshwm sim tias nws nyob nrog tus menyuam tau ntau xyoo lossis tseem phem dua - rau lub neej. Zoo siab yog cov niam txiv tsuas paub tias mob khaub thuas thiab qhov ntswg mus li cas. Peb yuav tsis tham txog cov teeb meem no hauv tsab xov xwm, peb yuav tham txog cov kab mob xws li mastocytosis hauv menyuam yaus.

mastocytosis nyob rau hauv cov me nyuam
mastocytosis nyob rau hauv cov me nyuam

Nkauj hais txog tus kab mob

Tus kab mob, thaum xub thawj siab ib muag, tsis ua rau muaj kev txhawj xeeb. Tab sis nws yog tsim nyog ncua nrog kev kho mob, mast hlwb pib sau nyob rau hauv tus me nyuam lub cev. Nyob rau tib lub sijhawm, tus kab mob tsis muaj mob tuaj yeem hloov mus rau hauv daim ntawv malignant.

Mastocytosis yog qhov tsawg heev, feem ntau cov menyuam yaus raug kev txom nyem los ntawm nws. Nws cuam tshuam tsis tau tsuas yog ntawm daim tawv nqaij, tab sis kuj rau lwm yam kabmob. Kwv yees li cuaj caum feem pua ntawm cov menyuam yaus uas muaj tus kab mob no raug kev txom nyem los ntawm urticaria pigmentosa. Thaum pib, yog tias mastocytosis raug kuaj pom hauv cov menyuam yaus, kev kho mob muaj nyob rau hauv kev siv cov tshuaj tiv thaiv. Nyob rau lub sijhawm noCov kab mob hauv qab no yuav tsum tau saib xyuas.

Nyob rau xya caum-tsib feem pua ntawm cov neeg mob, tus kab mob no tshwm sim rau cov menyuam yaus hnub nyoog qis dua peb xyoos thiab tsis nyob ntawm qhov sib deev ntawm tus menyuam. Lub etiology thiab pathogenesis tseem tsis tau kawm tag nrho, thiab nws yog tsis yooj yim sua kom meej lub npe ntawm qhov pib ntawm tus kab mob. Muaj kev xav tias qee zaum tus kab mob kis tau los ntawm txoj kev autosomal dominant.

Tim kab mob

Raws li tus yam ntxwv ntawm tus kabmob, mastocytosis hauv menyuam yaus thiab cov neeg laus muaj cov qauv hauv qab no.

mastocytosis hauv menyuam yaus ua rau
mastocytosis hauv menyuam yaus ua rau
  • Dermal, me nyuam mos. Pom tau hauv cov menyuam yaus txog peb xyoos. Tsis muaj kev puas tsuaj rau cov kabmob sab hauv. Cov pob khaus ntawm daim tawv nqaij ploj tag rau hauv kev puberty thiab tsis tshwm sim yav tom ntej. Nrog cov tsos mob hnyav, raug, thiab qhov tseem ceeb tshaj, yuav tsum tau kho raws sij hawm.
  • daim tawv nqaij mastocytosis hauv cov hluas thiab cov neeg laus. Kev puas tsuaj rau cov kabmob sab hauv tau pom, tab sis nrog daim ntawv no nws tsis ua tiav.
  • System. Feem ntau, hom kab mob no tshwm sim hauv cov neeg laus. Muaj kev hloov pauv ntawm daim tawv nqaij, kev puas tsuaj rau hauv lub cev.
  • Malignant form (mast cell leukemia). Daim ntawv ntawm tus kab mob no yuav luag tag nrho. Mast cells hloov. Lawv cuam tshuam rau hauv nruab nrog cev thiab cov ntaub so ntswg, tshwj xeeb tshaj yog cov pob txha thiab peripheral ntshav. Nws yuav tsum tau nco ntsoov tias daim tawv nqaij tshwm sim feem ntau tsis tuaj.

Nyob ntawm daim tawv nqaij lesions

Muaj tsib hom kab mob ntawm daim tawv nqaij.

  • Maculopapular mastocytosis hauv menyuam yaus. Ib daim duabqhia meej tias tus menyuam zoo li cas thaum lub sijhawm no. Tus me nyuam daim tawv nqaij yog tag nrho cov me me me thiab papules ntawm liab-xim av xim.
  • Ntau hom knotted. Muaj ntau lub pob tawv tawv ntawm daim tawv nqaij. Lawv tuaj yeem yog daj, liab, liab. Lawv txoj kab uas hla yog li ib centimeter, cov duab yog hemispherical.
  • Mastocytomas (tso leeg). Ib tug node tshwm. Nws txoj kab uas hla yog los ntawm ob mus rau tsib centimeters. Nws tuaj yeem ua tau du lossis wrinkled. Ib leeg mastocytosis nyob rau hauv cov me nyuam feem ntau tshwm sim nyob rau hauv lub cev, forearms, caj dab. Cov me nyuam mos feem ntau raug rau hom kab mob no.
  • Diffuse. Pib cuam tshuam cov menyuam yaus txij thaum ntxov. Cov kab mob daj-xim av tshwm rau ntawm daim tawv nqaij. Feem ntau lawv nyob hauv thaj tsam ntawm lub hauv caug, nruab nrab ntawm lub pob tw. Kev tawg tuaj yeem tshwm rau ntawm lawv.
  • Teleangiectatic yam. Tsis tshua muaj me nyuam.

Ua rau tus kab mob

Raws li tau hais los saum toj no, nws nyuaj heev los teb qhov twg tuaj yeem ua rau muaj tus kab mob txaus ntshai, vim nws tsis paub txog etiology. Tab sis tseem, nws muaj peev xwm txheeb xyuas cov laj thawj tseem ceeb uas ua rau mastocytosis hauv cov menyuam yaus. Komarovsky muab faib ua pawg raws li lub hnub nyoog ntawm tus me nyuam.

  • Nyob tshiab. Qhov ua rau tus kab mob tuaj yeem hu ua zaub mov tsis haum. Tus kws kho mob yuav tsum tau soj ntsuam yog tias tsev neeg tau raug tus kab mob no dhau los.
  • Me nyuam yaus hnub nyoog (los ntawm ib mus rau peb xyoos). Pab txhawb kom pom tus kab mob sib cuag nrog ib puag ncig.
  • Cov menyuam kawm ntawv preschools. Ntxiv rau tag nrho cov saum toj no yog vim li cas, ib qho kev tsis haum raukhoom ua si.
  • Cov menyuam kawm ntawv pib mob vim kev ntxhov siab, lub siab lub ntsws, kev ntxhov siab.
  • Cov tub ntxhais hluas feem ntau mob tom qab tawm hws ntau heev. Ib qho laj thawj yog kev cob qhia kis las.

Kev tiv thaiv tsis muaj zog yuav tsum raug ntaus nqi los ntawm qhov ua rau muaj tus kabmob. Thiab nws tseem yuav nthuav kom paub: yog tias ob peb tiam neeg mob hauv ib tsev neeg, nws tuaj yeem hais tau tias tus kab mob no yog keeb kwm ntawm xwm.

mastocytosis nyob rau hauv cov me nyuam yees duab
mastocytosis nyob rau hauv cov me nyuam yees duab

Cov tsos mob

Mastocytosis hauv cov menyuam yaus, zoo li txhua yam kab mob, muaj nws cov cim qhia. Cia peb tham txog lawv, txawm hais tias saum toj no, nyob rau hauv nqe lus "Cov hom kab mob ntawm daim tawv nqaij", peb twb tau tham txog cov tsos mob ntawm tus kab mob. Tab sis, raws li lawv hais, nws tsis mob kom nco qab.

Tsuas yog tus me nyuam muaj mob nthe, tsis xav ua si, nws yeej ib txwm npaj los nyob hauv nws niam nws txiv txhais caj npab, nws kuj muaj:

  • khaus khaus tshwm sim;
  • lub cev npog nrog cov pob liab liab;
  • redness hloov mus ua hlwv nrog cov kua ntshiab lossis ntshav;
  • pob khaus kis mus rau pob tw, ntsej muag, caj npab (yog tias tsis kho tam sim);
  • menyuam daim tawv nqaij thickens thiab yellowish.

Txoj kev ciam teb ntawm cov qauv uas tau tshwm sim tau txhais tau meej meej, qhov saum npoo tsis tev tawm. Ob peb hnub tom qab qhov tsos ntawm cov pob liab liab mus rau xim av tsaus.

Qee lub sij hawm kev loj hlob ntawm pob txuv tuaj yeem nres ntawm nws tus kheej, tab sis muaj qee lub sij hawm thaum tag nrho cov tawv nqaij raug cuam tshuam thiab lawv nkag mus rau hauv nruab nrog cev pib.

Sibform

YSolitary mastocytoma yog ib qho qog nqaij hlav uas tsim los ntawm mast cells. Hom kab no tsis tshua muaj, tab sis koj yuav tsum paub txog nws. Sawv cev ib leeg mastocytosis nyob rau hauv cov me nyuam (pom nyob rau hauv daim duab) qog tsim. Nws yog nyob rau ntawm lub cev, feem ntau nyob rau hauv lub nraub qaum, hauv siab, caj dab, forearm. Tsis tas yuav ntshai ua ntej. Kev txheeb cais qhia: hauv 90% ntawm cov xwm txheej, qhov stain no daws tau dhau sijhawm. Los ntawm kev puberty, tus menyuam yuav ploj mus tag. Hom kab mob no tsis yog tshwm sim los ntawm khaus khaus hnyav thiab cuam tshuam ntawm cov kab mob hauv nruab nrog cev.

Qee zaum ib daim ntawv ntawm mastocytosis tuaj yeem ua yuam kev rau cov xim nevus. Lawv coj tus menyuam mus rau tus kws phais kom tshem tawm qhov tsim. Nws yuav tsis ua rau tus menyuam zoo lossis daws qhov teebmeem.

Yog tus menyuam khawb lossis ua rau lub qhov txhab raug mob, npuas tshwm rau ntawm nws qhov chaw.

Diagnosis

Kuv yuav tsum hu rau leej twg los txiav txim qhov ua rau mastocytosis hauv menyuam yaus? Cov lus nug no txaus siab rau ntau tus niam txiv. Txawm li cas los xij, koj yuav tsum tsis txhob hnov qab mus ntsib kws kho mob tshwj xeeb. Nco ntsoov sab laj nrog kws kho mob dermatologist yog tias pom muaj pob nyob ntawm daim tawv nqaij ntawm tus menyuam. Nws yuav kuaj mob thiab, yog tias tsim nyog, xa mus rau nws cov npoj yaig. Txawm li cas los xij, tsis txhob pib kho koj tus kheej. Tom qab tag nrho, koj tsis paub meej tias yam twg ua rau muaj qhov tshwm sim ntawm pob khaus.

Mastocytosis nyob rau hauv cov me nyuam Komarovsky
Mastocytosis nyob rau hauv cov me nyuam Komarovsky

Tus kws kho mob yuav ua tib zoo tshuaj xyuas tus menyuam. Rau cov laj thawj no, feem ntau siv dermatoscope. Ua tsaug rau cov cuab yeej no, kev kuaj mob raug tshem tawm. Tom qab ntawdCov niam txiv yuav raug nug txog tus menyuam tus mob. Koj yuav tsum teb kom raug, nws yog ib qho tsim nyog yuav tsum nco ntsoov txhua qhov kev tsis txaus siab uas tuaj ntawm lub qhov ncauj ntawm tus menyuam. Tsis tas li ntawd, kev sim kuaj yuav raug ua. Koj yuav tau kuaj ntshav, kuaj xyuas ultrasound ntawm tag nrho cov kab mob hauv nruab nrog cev kom tsis suav nrog cov kab mob hauv lub cev.

mastocytosis hauv kev kho menyuam yaus
mastocytosis hauv kev kho menyuam yaus

Kev kho mob

Cov menyuam yaus kuaj mob mastocytosis. Cov laj thawj rau nws qhov tshwm sim, raws li qhov ua tau, raug txheeb xyuas. Nws yog lub sijhawm los pib kho. Cov txheej txheem tshwj xeeb tseem tsis tau tsim. Kev kho mob yog siv los txhim kho tus menyuam tus mob. Lub hom phiaj ntawm kev kho mob yog txo cov kev ua ntawm mast cell kev loj hlob. Cov me nyuam me thiab cov me nyuam loj dua raug tshuaj:

  • Tshuaj tiv thaiv kev tsis haum: "Suprastin", "Tavegil" thiab lwm yam.
  • Tshuaj muaj peev xwm ua kom ruaj khov ntawm kev ua txhaum ntawm cov hlwb.
  • PUVA therapy. Cov tawv nqaij yog kho nrog lub teeb ultraviolet. Nws yuav siv nees nkaum tsib zaug. Nws yog siv nyob rau hauv cov xwm txheej uas cov tshuaj antihistamines tsis ua hauj lwm. Cov txheej txheem yuav pab txo qhov chaw ntawm daim tawv nqaij.
  • Cytostatics (nrog rau daim ntawv ntawm tus kab mob). Tus kab mob nws tus kheej tsis tuaj yeem kho nrog lawv cov kev pab, tab sis nws muaj peev xwm ua kom qeeb thiab nres kev loj hlob ntawm mast cells.

Tom tau pom qhov ua rau mastocytosis hauv cov menyuam yaus, kev kho mob qee zaum tuaj yeem ua tiav siv cov zaub mov noj tshuaj.

mastocytosis hauv cov menyuam yaus ua rau kev kho mob
mastocytosis hauv cov menyuam yaus ua rau kev kho mob

Kev kho mob nrog pej xeem txoj kev

Peb ceeb toom koj tam sim ntawd, tshem tawm tus kab mob notxoj kev ua tau tsuas yog tom qab sab laj nrog kws kho mob. Nroj tsuag yuav pab txo qhov kev siv ntawm khaus thiab khaus ntawm daim tawv nqaij. Ntau yam zaub mov txawv:

  • Coriander (tshuaj ntsuab hmoov) yog tov nrog hmoov qab zib nyob rau hauv ib tug mus rau ib tug ratio. Haus ib nrab ib teaspoon ua ntej noj mov.
  • Ivy infusion. Ib diav ntawm Oak bark ntxiv rau ivy nplooj yog nchuav nrog boiling dej (ib liter) thiab infused kom txog thaum txias. Ib tug compress yog ua. Nyob ntev nees nkaum feeb ntawm thaj chaw cuam tshuam.
  • Infusion ntawm nettles. Ib tablespoon ntawm qhuav nettle yog noj. Ncuav nyob rau hauv ib khob ntawm boiled dej. Cov chaw uas muaj kab mob yog rubbed nrog cov tshuaj no ob peb zaug hauv ib hnub.
  • Mastocytosis hauv cov menyuam yaus kuj tau kho nrog tshuaj ntsuab da dej. Thaum da dej, cov hauv qab no ntxiv rau hauv dej: chamomile, celandine, nettle, sage thiab hlua.

Siv cov hau kev no yuav tsis muaj peev xwm tshem tau tus menyuam qhov teeb meem tag nrho, tab sis tus mob yuav ua kom yooj yim dua.

Txoj kev mob tshwm sim

Nws tau rov hais dua ob peb zaug thoob plaws hauv kab lus: yog tias koj pom pob pob liab liab ntawm tus menyuam lub cev, nrog rau tus kws kho mob tam sim ntawd. Tom qab tag nrho, tus kab mob uas tsis muaj kev phom sij tuaj yeem ua rau muaj teeb meem loj dua: kev puas tsuaj ntawm lub cev thiab kev tuag.

Kev ntsuas tus kab mob nyob ntawm qhov ua rau mastocytosis hauv cov menyuam yaus. Daim duab qhia tau hais tias cov teeb meem feem ntau ploj mus ntawm lawv tus kheej thiab tsis muaj qhov chaw nyob ntawm tus menyuam lub cev.

mastocytosis nyob rau hauv cov me nyuam ua rau cov duab
mastocytosis nyob rau hauv cov me nyuam ua rau cov duab

Cov lus xaus no tsis tuaj yeem ua nrog qhov mob ntawm lub cev. Yog tias mast cell leukemia raug kuaj pom, nws tsis tsim nyog tham txog kev loj hlob zoo. Yog vim li ntawd duaPeb rov hais dua: tsis txhob ncua kev kho mob. Nrhiav kev kho mob tam sim.

Pom zoo: