Yuav ua li cas thiaj tshem tau Gilbert's syndrome?

Yuav ua li cas thiaj tshem tau Gilbert's syndrome?
Yuav ua li cas thiaj tshem tau Gilbert's syndrome?

Video: Yuav ua li cas thiaj tshem tau Gilbert's syndrome?

Video: Yuav ua li cas thiaj tshem tau Gilbert's syndrome?
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Anonim

Tus kab mob no cuam tshuam txog kab mob tshwj xeeb, uas yog tus cwj pwm los ntawm kev nce qib ntawm bilirubin hauv cov ntshav, jaundice, thiab qee cov tsos mob. Raws li cov kws tshaj lij, thaum kuaj pom Gilbert's syndrome, tsis muaj kev phom sij rau kev noj qab haus huv ntawm tus neeg mob nws tus kheej thiab tib lub sijhawm xav tau kev kho tshwj xeeb. Cia peb saib cov tsos mob tseem ceeb thiab kev kho mob rau tus kab mob.

Gilbert's Syndrome
Gilbert's Syndrome

Dab tsi ua rau Gilbert's syndrome?

Cov kws tshawb fawb tau muaj peev xwm ua pov thawj tias tus kab mob no tshwm sim vim qhov tsis txaus ntawm lub siab enzyme tshwj xeeb (lub npe hu ua glucuronyl transferase), uas ncaj qha koom nrog cov metabolism hauv bilirubin. Qhov teeb meem no feem ntau yog tshwm sim los ntawm cov yam ntxwv ntawm caj ces ntawm tus neeg. Yog li, nrog rau qhov tsis muaj cov enzyme no hauv daim siab, tsis muaj kev cuam tshuam ntawm kev tsis ncaj ncees bilirubin, uas thaum kawg ua rau nws nce thiab kev loj hlob tom qab ntawm jaundice.

Lub hnub nyoog twg yog Gilbert's syndrome kuaj pom?

Raws li cov kws tshaj lij hauv qhov teeb meem no tau lees paub, nce qib ntawm bilirubin nws tus kheejtuaj yeem pom thaum yug los. Txawm li cas los xij, yuav luag txhua tus menyuam mos, qhov ntsuas no siab dua li qhov ntsuas me ntsis, uas ua rau muaj kev kuaj mob lig.

Gilbert's Syndrome genetic tsom xam
Gilbert's Syndrome genetic tsom xam

Cov tsos mob tseem ceeb

Ua ntej tshaj plaws, nws yuav tsum raug sau tseg tias cov kws kho mob tsis paub qhov txawv ntawm cov tsos mob mus tas li thaum kuaj Gilbert's syndrome. Qhov no txhais tau tias lawv tuaj yeem tshwm sim hauv ntau qhov xwm txheej. Piv txwv li, tom qab kev tawm dag zog lub cev, ua rau muaj kev ntxhov siab, vim yog kev noj ntawm qee pawg tshuaj lossis cov khoom siv cawv. Txawm li cas los xij, cov kws tshaj lij tseem txheeb xyuas cov yam ntxwv zoo tshaj plaws uas qhia tias muaj tus kab mob. Cov no suav nrog cov hauv qab no:

  • qaug zog thiab qaug zog tas li;
  • Jaundice ntawm daim tawv nqaij thiab cov ntaub nyias nyias nyias;
  • tas li tsis xis nyob hauv txoj cai hypochondrium.

Diagnosis

Raws li tau sau tseg saum toj no, qhov taw qhia tseem ceeb ntawm tus mob no yog qib siab ntawm bilirubin vim qhov hu ua feem tsis ncaj. Cov kws kho mob tshwj xeeb tshaj tawm rau cov kab mob xws li Gilbert's syndrome, kev tshuaj ntsuam genetic tsom xam thiab ntau qhov kev ntsuam xyuas ntxiv, suav nrog kev sim nrog phenobarbital.

Gilbert's Syndrome noj zaub mov
Gilbert's Syndrome noj zaub mov

Kev kho mob

Tam sim no, cov kws kho mob paub tseeb tias tus kab mob no tsis xav tau kev kho mob tshwj xeeb, tsuas yog qee cov lus pom zoo yuav tsum ua raws. Tom qab ntawd, qib bilirubin yuav rov zoo li qub, thiab cov tsos mob yuav ploj mus tag nrho. Yog li, hom hauv qhov no txhais tau tiasraws li qhov siab tshaj plaws ntawm kev tawm dag zog lub cev. Raws li kev kho tshuaj, qee zaum cov kws tshaj lij pom zoo kom noj qee cov tshuaj uas muaj lub luag haujlwm los txhim kho lub siab ua haujlwm tseem ceeb (piv txwv li, Karsil, Hofitol, Heptral, thiab lwm yam).

YGilbert's Syndrome. Kev noj haus

Kev noj zaub mov tshwj xeeb ua lub luag haujlwm tshwj xeeb hauv kev tshem tawm cov tsos mob tsis xis nyob. Nws txhais tau hais tias kev cais tawm tag nrho los ntawm kev noj zaub mov muaj rog thiab cov khoom siv cawv. Nyob rau hauv tsis muaj cov ntaub ntawv yuav tsum tau cov neeg mob tshaib plab, yog li ntawd, nws yog pom zoo kom ua ib tug me me lub sij hawm ntawm noj mov. Noj qab nyob zoo!

Pom zoo: