Amblyopia, lossis McKusick-Kaufman syndrome, yog qhov tsis pom kev tsis pom kev. Qhov no tsis cuam tshuam nrog cov kab mob organic ntawm cov tshuaj ntsuam xyuas thiab tsis tuaj yeem hloov kho kho qhov muag. Hauv tsab xov xwm no, peb yuav xav txog tus kab mob kom ntxaws ntxiv.
Kaufman syndrome cov tsos mob
Hnub ntawm tus mob no yuav yog asymptomatic, lossis nws yuav tsis tuaj yeem kho qhov ntsia. Kev xaav ntawm cov xim kuj cuam tshuam, muaj teeb meem nrog kev taw qhia hauv qhov chaw. Feem ntau, qhov pom kev acuity raug txo. Kev kuaj mob ntawm tus kab mob suav nrog kev tsim kom pom qhov pom kev pom thiab pom xim xim. Cov kws kho mob kuj tshuaj xyuas cov fundus, ua tonometry, thiab lwm yam. Kev kho mob ntawm tus mob yog tsom rau kev tshem tawm cov laj thawj uas ua rau nws txoj kev loj hlob. Nyob rau hauv cov ntaub ntawv no, kev phais los yog kev kho mob yog ua tau. Cov ntsiab lus ntxiv txog cov kev xaiv rau kev kuaj mob Kaufman syndrome, nrog rau cov kev kho mob, yuav tau tham hauv qab no.
Ntau yam kab mob
Cov kab mob no tseem hu ua tus mob " ruam", lossis lwm yam lus, "tub nkeeg" qhov muag, uas yog tus cwj pwm los ntawm kev tsis ua haujlwm, nrog rau tsis muaj kev koom tes hauv cov txheej txheem ntawm kev pom. Hauv ophthalmology, qhov noTus kab mob no suav tias yog ib qho ntawm cov laj thawj tseem ceeb ntawm unilateral deterioration ntawm tib neeg lub zeem muag.
Kaufmann's Syndrome yog tshwm sim los ntawm cov kab mob hauv lub cev thiab kev loj hlob thiab kev loj hlob retardation.
Thoob ntiaj teb, cov kab mob no cuam tshuam txog li ob feem pua ntawm cov pej xeem. Tus kab mob no yog ib hom mob feem ntau ntawm cov menyuam yaus. Nws yog vim li no tias qhov tseem ceeb zoo li no tau txais kev xav tau ntawm nws qhov kev tshawb pom ntxov thiab kho.
Syndrome Diagnosis
txhawm rau kuaj Kauffman's syndrome, yuav tsum tau kuaj pom tus neeg mob. Raws li ib feem ntawm qhov kev ntsuam xyuas qhov muag thawj zaug, tus kws kho qhov muag tig nws lub ntsej muag feem ntau rau daim tawv muag, thiab, ntxiv rau, mus rau palpebral fissure. Tsis tas li ntawd, ib qho yuav tsum tau coj mus rau hauv tus account qhov chaw ntawm lub qhov muag thiab txiav txim siab cov tshuaj tiv thaiv ntawm cov menyuam kawm ntawv rau lub teeb. Daim duab dav dav ntawm lub xeev tsis pom kev tuaj yeem tau txais los ntawm kev kuaj mob ophthalmological:
- Lub ntse yog kuaj tsis tau kho, nrog rau nws cov keeb kwm yav dhau.
- Kev kuaj xim tab tom ua.
- Perimetry tab tom ua, uas yog qhov kev ntsuas kev cuam tshuam.
Raws li qhov txo qis ntawm qhov pom kev pom hauv tus neeg mob, qhov ntsuas qhov hnyav ntawm Kaufman's syndrome tau txiav txim siab. Kev kuaj mob yuav tsum tau raws sijhawm.
Txhawm rau tshuaj xyuas cov qauv ntawm lub qhov muag, ophthalmoscopy thiab biomicroscopy tau ua, ntxiv rau, kev tshawb fawb hauv qab ntawm qhov pom ntawm lub cev siv lub lens Goldman. Txhawm rau tsim kom muaj qhov pom tseeb ntawm cov xov xwm refractive, uas yog lub lens thiab cov vitreous, sivkev ntsuam xyuas lub qhov muag nyob rau hauv lub teeb kis. Tawm tsam keeb kwm yav dhau los ntawm opacity ntawm kev tshaj tawm, lawv tus mob yuav tsum tau kuaj nrog kev kuaj ultrasound ntawm lub qhov muag.
Ntawm cov kev xaiv biometric rau kev tshawb fawb, lub luag haujlwm tseem ceeb tshaj plaws yog ua los ntawm kev tsim lub kaum sab xis ntawm strabismus raws li Hirshberg nrog rau kev ntsuas ntawm qhov ntsuas no ntawm lub synaptophore. Txhawm rau kom tsis suav cov refractive, nrog rau anisometropic hom amblyopia, cov kev tshawb fawb txog kev cuam tshuam tau raug sau tseg, xws li skiascopy thiab refractometry. Raws li ib feem ntawm kev ntsuam xyuas dav dav ntawm cov neeg mob uas muaj tus kab mob no, tonometry lossis electroretinography tuaj yeem suav nrog. Yog tias tsim nyog, nrog Kauffman's syndrome, koj yuav tsum sab laj nrog kws kho mob hlwb.
Techniques and treatment options
Tsuas yog thaum ntxov, xaiv tus kheej, ntxiv rau, kev kho mob tsis tu ncua tuaj yeem muab cov txiaj ntsig zoo. Kev kho yog qhov zoo tshaj plaws ua ntej muaj hnub nyoog rau rau rau xya xyoo. Hauv cov menyuam yaus hnub nyoog qis dua kaum ib mus rau kaum ob xyoos, Kaufman's syndrome yog qhov kho tsis tau.
Kev ua tiav ntawm kev kho qhov muag ntawm cov kab mob cuam tshuam ncaj qha rau kev tshem tawm ntawm nws qhov ua rau. Yog li, nrog rau hom obscurative ntawm amblyopia, cov kev kho mob hauv qab no yuav tsum tau:
- Kev tshem tawm kab mob cataract.
- Kev phais kho ptosis.
- Kev kho mob nqus tau.
- Kev ua haujlwm vitrectomy rau hemophthalmos.
Kev kho phais
Nyob rau hauv qhov xwm txheejdysbinocular hom amblyopia, phais kho ntawm strabismus yog ua. Kev kho mob ntawm daim ntawv refractive los yog anisometropic ntawm tus kab mob yog nqa tawm los ntawm kev saib xyuas. Thaum pib, raws li txoj cai, kev kho qhov muag pom kev zoo tau raug sau tseg. Tib lub sijhawm, ua tib zoo xaiv cov iav thiab lo ntsiab muag. Tawm tsam keeb kwm ntawm anisometropia, kev kho laser yog ua.
Pleoptics
Txog peb lub lis piam tom qab, kev kho mob pleoptic pib, uas lub hom phiaj txhawm rau tshem tawm lub luag haujlwm tseem ceeb ntawm lub cev pom qhov pom zoo. Nws tseem yog ib qho tseem ceeb kom qhib lub qhov muag ntawm amblyopic. Rau kev kho mob ntawm Kaufman's syndrome, nquag siv, ntxiv rau, kev siv cov pleoptics passive.
Passive cuam tshuam nrog kev sib khi thiab occlusion ntawm lub qhov muag ua ntej. Lub active hom, nyob rau hauv lem, combines lub occlusion ntawm lub qhov muag pom lub cev nrog kev ua tau zoo ntawm retinal stimulation ntawm lub qhov muag tsis zoo. Stimulation yog tsim los ntawm lub teeb thiab hluav taws xob impulses. Cov khoos phis tawj tshwj xeeb kuj tau siv.
Hardware method
Ntawm cov txheej txheem kho vajtse, kev kho mob ntau tshaj plaws rau tus kab mob no yog kev cob qhia ntawm Amblyocore, nrog rau cov kev kho mob hauv qab no:
- Kev ua haujlwm laser stimulation.
- Kev siv lub teeb xim stimulation thiab hluav taws xob stimulation.
- Kev ua haujlwm ntawm electromagnetic stimulation.
- Kev vibration stimulation nrog rau kev txhawb nqa.
- Ntau hom kev txhawb nqa hauv computer.
Cov chav kawm Pleoptic yuav tsum tau rov ua peb mus rau plaub zaug hauv ib xyoos. Hauv menyuam yauscov menyuam yau, uas tsis muaj hnub nyoog tshaj plaub xyoos, raug kho nrog kev pab ntawm kev nplua, uas yog lub hom phiaj kev puas tsuaj rau lub zeem muag ntawm lub cev tseem ceeb vim yog kev teem caij ntawm hypercorrection. Cov tshuaj Atropine kuj yuav raug sau tseg. Hauv qhov xwm txheej no, qhov pom kev acuity ntawm lub qhov muag ua tau raug txo qis, uas tau ua rau kev ua kom lub cev tsis muaj zog. Nrog rau qhov mob no, txoj kev kho lub cev muaj txiaj ntsig tshwj xeeb. Yog li, cov kev kho mob xws li reflexology yog qhov tsim nyog tshwj xeeb, nrog rau kev vibration massages thiab tshuaj electrophoresis.
Kev pom kev kho dua tshiab
Tom qab theem pleoptic ntawm kev kho, raws li txoj cai, lawv mus rau kev kho dua tshiab ntawm lub zeem muag. Rau qhov no, kho orthodontic yog siv. Nws raug nquahu kom ua qhov theem no thaum tib lub qhov muag pom kev ua tiav ntawm ob lub qhov muag. Hauv qhov no, lub hnub nyoog ntawm tus menyuam yuav tsum tsis pub tsawg tshaj plaub xyoos. Feem ntau, rau lub hom phiaj no, ib qho cuab yeej siv - ib qho synoptophore, los ntawm cov eyepieces uas tus neeg mob tswj xyuas kom pom cov seem ntawm tag nrho cov duab, lawv yuav tsum tau pom kev sib xyaw ua ke rau hauv ib daim duab.
Kaufman's syndrome raug kho kom txog thaum kwv yees li qhov sib npaug ntawm qhov pom ntawm ob qho tib si hauv nruab nrog cev. Cov neeg mob kuj tuaj yeem muab tshuaj sedatives, thiab kev kho mob hlwb yuav tsis ua rau muaj kev ntxhov siab.
