Madelung syndrome: ua rau, kho thiab tiv thaiv

Cov txheej txheem:

Madelung syndrome: ua rau, kho thiab tiv thaiv
Madelung syndrome: ua rau, kho thiab tiv thaiv

Video: Madelung syndrome: ua rau, kho thiab tiv thaiv

Video: Madelung syndrome: ua rau, kho thiab tiv thaiv
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Anonim

Ob lub puab tsaig yog qhov tsis xws luag uas tuaj yeem cuam tshuam nrog cov kab mob metabolic lossis rog rog. Qee lub sij hawm nws tsuas yog ib qho tshwj xeeb ntawm lub cev. Tab sis qee zaum, qhov nce ntxiv ntawm cov rog hauv lub cev yog pov thawj ntawm tus kab mob Madelung loj. Cov mob no yuav tsis ua rau lub neej hem, tab sis ua rau kev loj hlob ntawm kev puas siab puas ntsws complexes.

Tus yam ntxwv ntawm tus kab mob

Ib hom lipomatosis yog Madelung tus kab mob. Cov tsos mob tshwm sim vim yog ua txhaum ntawm cov txheej txheem metabolic hauv lub cev, vim tias cov rog tsis tau muab faib kom raug, ntau qhov tso nyiaj tshwm sim hauv caj dab.

Tus mob no tau piav qhia thawj zaug hauv xyoo 1888 los ntawm tus kws kho mob Madelung - yog li lub npe sib xws.

Madelung Syndrome
Madelung Syndrome

Ib lipoma tshwm rau ntawm caj dab, uas maj mam nce, mus txog qhov loj me. Yog tias koj tsis nrhiav kev kho mob raws sijhawm, Madelung's syndrome yuav ua rau tus neeg mob tsis tuaj yeem tig nws lub caj dab, qhov mob yuav tshwm sim.

Rau qhov ntau dua, cov neeg laus ntawm ob leeg poj niam cev xeeb tub raug tus kab mob no. Hauv cov menyuam yaus, pathology yog xyaum tsis kuaj.

Yog vim li cas

Vim li cas Madelunga (tus mob) tshwm sim? Yog lus teb rau qhov nonug hnub no tsis muaj leej twg ua tau. Txawm li cas los xij, muaj ntau yam uas tuaj yeem ua rau kev loj hlob ntawm pathology:

  1. Heredity feem ntau raug xa mus rau ntawm no. Yog tias qhov pathology no tau pom nyob rau hauv leej txiv lossis leej niam, nws muaj peev xwm tsim cov rog zoo sib xws tom qab ncav cuag ib lub hnub nyoog ntawm tus menyuam.
  2. Tsis tas li ntawd, hormonal ntshawv siab nyob rau hauv lub cev tuaj yeem ua qhov ua rau muaj tus kab mob.
  3. Cov neeg haus cawv thiab quav yeeb quav tshuaj muaj kev pheej hmoo.
  4. Kev ua txhaum ntawm cov txheej txheem metabolic hauv lub cev tuaj yeem ua rau muaj kev ntxhov siab thiab ntxhov siab. Feem ntau lipomatosis, suav nrog Madelung's syndrome, kev kho mob uas yuav tsum tau ua tshwj xeeb, raug kuaj pom hauv cov poj niam uas niaj hnub noj zaub mov. Raws li qhov tshwm sim ntawm kev noj zaub mov tsis txaus, rog pib tso rau hauv qhov tsis raug.
Kev kho mob ntawm Madelung Syndrome
Kev kho mob ntawm Madelung Syndrome

Symptomatics

Thawj zaug, tus neeg mob yuav pom muaj ntau cov rog rog hauv cov qog nqaij hlav ntawm caj dab. Hmoov tsis zoo, nyob rau theem no, ob peb tus neeg muab qhov tseem ceeb rau cov tsos mob tsis zoo yam tsis tau nrhiav kev pab kho mob. Hauv ob peb lub hlis, lub caj dab tuaj yeem nce qhov loj me. Qhov tshwm sim yog ua pa luv thiab mob.

Madelung Syndrome kho thiab cov tsos mob
Madelung Syndrome kho thiab cov tsos mob

Yog tias cov ntaub so ntswg adipose hlob mus rau hauv cov txheej txheem sib sib zog nqus ntawm cov epidermis, nrog cov tsos mob tshwm sim xws li tachycardia, mob taub hau, qaug dab peg.

Yog tias muaj ib qho laj thawj, nws tsim nyog kawm kom paub meejhais txog Madelung's Syndrome. Kev kho mob thiab cov tsos mob, txoj kev tiv thaiv - tag nrho cov ntaub ntawv no tseem ceeb.

Kev kho mob

Kev kuaj mob raws sijhawm yog qhov tseem ceeb, uas tso cai rau txiav txim siab vim li cas cov ntaub so ntswg adipose pib loj hlob sai. Raws li cov ntaub ntawv tau txais, tus kws kho mob tshwj xeeb tshaj tawm cov kev kho mob uas muaj hormonal, detoxifying thiab anti-inflammatory tshuaj. Tab sis nws yuav tsis muaj peev xwm tshem tau cov wen loj yam tsis muaj kev phais, yog li tus neeg mob tau npaj rau kev phais.

Madelung Syndrome tiv thaiv
Madelung Syndrome tiv thaiv

Muaj ntau ntau txoj hauv kev los tshem tawm lipomas loj ntawm caj dab. Txoj kev siv yooj yim tshaj plaws thiab pheej yig tshaj yog kev txiav tawm yooj yim raws li kev siv tshuaj loog. Cov haujlwm no tau ua nyob rau hauv ntau lub tsev kho mob pej xeem. Tab sis kev phais yog suav tias yog mob heev. Nrog rau cov roj deposits loj, muaj qhov yuav ua rau caws pliav thiab caws pliav. Thiab tsis pub dhau ob peb hnub tom qab ua haujlwm, tus neeg mob tau muab tshuaj tua kab mob kom tsis txhob kis kab mob.

Endoscopic tshem tawm ntawm lipomas ntawm caj dab yog suav tias tsis tshua muaj mob. Txawm li cas los xij, cov txheej txheem no tsuas yog tsim nyog yog tias muaj cov rog me me. Hauv cov chaw kho mob ntiag tug, kuv kuj xyaum kev phais mob siv lub laser.

Hmoov tsis zoo, kev tshem tawm ntawm kev tsim kho tsis zoo tsis yog kev lees paub tias Madelung's syndrome yuav tsis rov qab los yav tom ntej. Kev tiv thaiv ntawm relapses muaj nyob rau hauv kev tsis lees paub cov khoom noj muaj roj ntau thiab cawv, nrog rau kev tswj hwm.noj qab nyob zoo txoj kev ua neej nyob rau hauv dav dav. Nws yuav kho tau tus kab mob sai dua yog tias koj nrhiav kev pab thaum ntxov.

Pom zoo: