Enzyme deficiency: hom, ua tau, cov tsos mob thiab kev kho mob

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Enzyme deficiency: hom, ua tau, cov tsos mob thiab kev kho mob
Enzyme deficiency: hom, ua tau, cov tsos mob thiab kev kho mob

Video: Enzyme deficiency: hom, ua tau, cov tsos mob thiab kev kho mob

Video: Enzyme deficiency: hom, ua tau, cov tsos mob thiab kev kho mob
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Anonim

Lo lus "enzymatic deficiency" yog hais txog cov kab mob pathological uas cov enzymes tsim tawm tsis sib haum rau qhov xav tau tiag tiag ntawm lub cev. Qhov tsis muaj cov tshuaj lom neeg lom neeg ua rau muaj kev cuam tshuam ntawm cov txheej txheem digestive. Enzymatic deficiency tsis yog kab mob ywj pheej. Qhov no yog ib qho kev ceeb toom uas qhia txog kev loj hlob ntawm pathology loj hauv lub cev. Tsis quav ntsej tus kab mob ua rau muaj teeb meem.

Kev txhim kho mechanism

Nquag, kab mob plab hnyuv tsim cov tshuaj lom neeg lom neeg - enzymes uas ncaj qha rau hauv cov txheej txheem zom zaub mov. Raws li kev cuam tshuam ntawm ntau yam tsis zoo, muaj qhov txo qis hauv kev tsim cov enzymes. Yog li ntawd, lub cev tsis tau txais cov enzymes nyob rau hauvxav tau.

Cov kws kho mob paub qhov txawv 2 hom kab mob: gastrogenous thiab pancreatic. Hauv thawj kis, enzymatic deficiency yog vim qhov txo qis hauv kev tsim cov kua txiv hmab txiv ntoo. Daim ntawv pancreatic tsim tawm tsam keeb kwm yav dhau ntawm cov kab mob pancreatic pathologies.

Kev tsim cov enzymes
Kev tsim cov enzymes

Yog vim li cas

Tus kab mob tuaj yeem tshwm sim los ntawm ntau yam ua rau muaj kev cuam tshuam. Lub ntsiab yog vim li cas rau kev loj hlob ntawm enzyme deficiency:

  • Nquag noj zaub mov ntau. Raws li qhov tshwm sim, lub plab zom mov tsis tuaj yeem tiv taus thiab tsis tuaj yeem tsim cov enzymes kom raug.
  • Pancreatitis, mob hnyav thiab mob ntev.
  • kab mob kab mob.
  • Neoplasms ntawm ob qho tib si benign thiab malignant xwm.
  • Qhov muaj pob zeb hauv lub gallbladder, ua rau ua txhaum ntawm kev tawm ntawm pancreatic secretion.
  • Hypoacid gastritis, tawm tsam uas tsim cov enzymes digestive thiab hydrochloric acid txo.
  • Muaj cov txheej txheem inflammatory hauv plab thiab / lossis cov hnyuv me (gastritis, gastroenteritis, enteritis).
  • Pathology ntawm daim siab thiab gallbladder.
  • Crohn's disease.
  • kab mob autoimmune.
  • Amyloidosis.
  • noj tsis sib haum.
  • Nyem ua raws li kev noj zaub mov nruj.
  • Kev phais mob hauv lub cev ntawm lub plab zom mov.

Feem ntau qhov ua rau ntawm kev loj hlob ntawm enzymatic insufficiency ntawm pancreas yog congenital anomalies. Hauv cov xwm txheej zoo li no, kev kho mob tshwm sim sai sai tom qab yug menyuam.

Pancreas
Pancreas

hom mob

Tus kab mob tuaj yeem muaj tus cwj pwm txawv. Hom enzymatic deficiency nyob rau hauv cov neeg laus thiab cov me nyuam yog tsim nyob rau hauv lub diagnostic theem yam tsis poob. Qhov kev xav tau no yog vim qhov tseeb tias txhua hom kab mob yuav tsum muaj qee yam hauv kev kho mob.

Type of deficiency:

  1. Sab nraud secretory. Nws tsim tawm tsam keeb kwm yav dhau los ntawm kev ua txhaum ntawm kev tso tawm ntawm cov kua dej tso rau hauv duodenum, nrog rau kev txo qis hauv qhov loj ntawm exocrine parenchyma. Kev ua haujlwm tsis zoo ntawm lub plab zom mov ua rau lub cev hnyav heev.
  2. Exocrine. Hom no tshwm sim nyob rau hauv lub xub ntiag ntawm cov kab mob nyob rau hauv lub txiav, uas yog irreversible. Feem ntau, enzyme deficiency tshwm sim nyob rau hauv cov neeg uas tsis kho cov kab mob ntawm lub digestive system, nrog rau cov neeg uas noj cov zaub mov uas muaj rog thiab haus dej haus cawv.
  3. YEnzymatic. Qhov ua rau muaj tus kab mob no yog kev tswj tsis tau thiab siv sijhawm ntev ntawm cov tshuaj, cov khoom siv uas ua rau muaj kev cuam tshuam tsis zoo rau cov ntaub so ntswg ntawm tus txiav.
  4. Endocrine. Nws tshwm sim thaum lub caj pas ua lub luag haujlwm rau kev tsim cov tshuaj insulin, lipocaine thiab glucagon puas lawm. Hauv cov xwm txheej zoo li no, ntshav qab zib mellitus tshwm sim ib txhij nrog enzyme deficiency.

Yog li, tus kab mob muaj ntau hom. Lub luag haujlwm tseem ceeb ntawm tus kws kho mob yog txiav txim siab kom raug thiabkos cov kev kho mob zoo tshaj plaws.

Cov enzymes digestive
Cov enzymes digestive

Symptoms

Enzymatic deficiency yog ib qho mob, qhov kev kho mob tshwm sim uas ncaj qha nyob ntawm nws hom.

Tus kab mob exocrine muaj cov tsos mob hauv qab no:

  • Zoo plab plab. Lawv tshwm sim tom qab noj cov zaub mov muaj roj, nrog rau cov khoom noj uas muaj txuj lom.
  • Bloating.
  • xav hnyav hauv plab.
  • Zoo plab. Tib lub sijhawm, cov rog uas tsis tau nqus los ntawm lub cev tuaj yeem pom hauv cov quav.
  • mob plab plab. Raws li txoj cai, lawv tawg mus rau sab.
  • daim tawv nqaij qhuav. Lawv kuj coj ib tug grey tint.
  • High heart rate.
  • ua tsis taus pa.

Cov tsos mob ntawm pancreatic enzyme deficiency (exocrine daim ntawv):

  • Ntsuab tig los ntuav.
  • Meteorism.
  • quav quav.
  • Cov quav quav.
  • Ntsuag.
  • Pab pw tsis tsaug zog.
  • Apathy.

hom Enzymatic deficiency muaj cov tsos mob hauv qab no:

  • Rumbling thiab seething hauv plab.
  • Zoo.
  • poob phaus.
  • Nkauj qab zib.
  • Zoo siab.
  • Zoo pib ntawm qaug zog.
  • Nkauj kho siab.

Cov tsos mob ntawm endocrine enzyme deficiency:

  • Ntau zaus raws plab.
  • Nkauj tshwm sim ntuav ntuav.
  • Kev poob phaus.
  • Tsis qab los noj.
  • Burp.
  • Bloating.
  • Zoo siab.
  • Psycho-emotional instability.
Cov tsos mob tsis txaus
Cov tsos mob tsis txaus

Tus yam ntxwv ntawm tus kabmob hauv menyuam yaus

Nyob rau hauv cov menyuam mos, pathology tsim nyob rau hauv kev cuam tshuam ntawm ob qho tib si sab nraud thiab sab hauv provoking yam. Qhov laj thawj tseem ceeb ntawm kev tsis txaus enzyme hauv cov menyuam yaus:

  • Gene defects.
  • Kab mob pancreas.
  • Pathology ntawm tus kab mob sib kis.
  • YKev ua txhaum ntawm plab hnyuv microflora.
  • Kev siv tshuaj tsis raug cai.
  • noj tsis sib haum.
  • Nyob hauv cheeb tsam uas tsis zoo ib puag ncig.

Cov tsos mob ntawm cov enzyme deficiency hauv cov me nyuam mos tshwm sim sai tom qab yug me nyuam. Cov cim hauv qab no yog qhov ceeb toom:

  • Cov quav quav.
  • Tsis qab los noj.
  • Ntsuab tig los ntuav.
  • Kev poob phaus.
  • Bloating.
  • Nyob hauv plab.

Ntxiv rau, nrog rau qhov tsis muaj enzyme hauv cov menyuam yaus, muaj qhov qeeb qeeb hauv kev loj hlob ntawm lub cev. Yog tias cov cim ceeb toom saum toj no tshwm sim, koj yuav tsum qhia tus menyuam mos tam sim ntawd rau tus kws kho mob.

Hauv cov menyuam yaus tom qab ib xyoos, enzymatic deficiency yog tshwm sim los ntawm kev noj zaub mov tsis zoo lossis kev qhia tsis raug ntawm cov khoom noj ntxiv. Nyob rau tib lub sijhawm, cov menyuam yaus muaj cov tsos mob zoo ib yam li cov menyuam yug tshiab. Nrog sijhawmtxheeb xyuas tus kab mob txaus los noj tshuaj thiab kho cov zaub mov. Kev kho mob yuav tsum tau ua los ntawm kws kho menyuam yaus lossis kws kho mob plab.

Pathology nyob rau hauv cov me nyuam
Pathology nyob rau hauv cov me nyuam

Diagnosis

Enzymatic deficiency, uas yog keeb kwm, feem ntau tau kuaj pom twb nyob rau theem ntawm kev kuaj menyuam mos. Hauv cov neeg laus, pathology raug kuaj pom thaum kuaj mob lossis tom qab tus neeg tau mus ntsib kws kho mob nrog ntau qhov kev tsis txaus siab.

txhawm rau txheeb xyuas thiab lees paub qhov kev kuaj mob, tus kws kho mob tau tshaj tawm kev kuaj xyuas, suav nrog:

  • ultrasound;
  • duodenal suab;
  • kuaj ntshav biochemical;
  • quav quav thiab tso zis.

Yog tias muaj qhov tsis txaus enzyme, tus kws kho mob tshwj xeeb tau txais kev kho mob.

Kev kho mob

Kev tshem tawm tus kab mob yuav tsum muaj kev sib koom ua ke. Txoj kev kho mob rau kev tsis txaus enzyme ncaj qha nyob ntawm qhov ua rau ntawm txoj kev loj hlob ntawm pathology thiab nws qhov hnyav. Yog tias tus kab mob yog qhov tshwm sim ntawm kev loj hlob ntawm neoplasms, nws yog thawj zaug uas yuav tsum tau tshem tawm cov qog. Nyob rau hauv tus txheej txheem ntawm kev phais, tsis tsuas yog pathologically hloov hlwb, tab sis kuj yog ib feem ntawm lub cev yuav excised.

Yog tias qhov ua rau tsis txaus yog ntshav qab zib mellitus, pancreatitis lossis lwm yam mob uas tsis tas yuav kho phais, tus neeg mob tau pom tias noj cov tshuaj, cov khoom nquag uas ua rau cov enzymes hauv lub cev normalizes. Raws li txoj cai, cov kws kho mob tau sau cov tshuaj hauv qab no: Creon, Mezim, Pancreatin.

Cov tshuaj noyog cov tsiaj keeb kwm, txij li lawv cov khoom muaj txiaj ntsig yog cov txheej txheem pancreas coj los ntawm nyuj. Feem ntau, thaum noj cov tshuaj no, cov neeg mob ntsib kev tsis haum tshuaj. Nyob rau hauv xws li mob, tus kws kho mob sau tshuaj ntsuab npaj. Nws yog tsim nyog sau cia tias lawv cov txiaj ntsig qis dua.

Kev kho mob ntawm tus kab mob
Kev kho mob ntawm tus kab mob

Khoom noj khoom haus

Kev kho tshuaj yuav tsis ua rau muaj txiaj ntsig zoo yog tias tus neeg mob tsis ua raws li kev noj haus. Kev kho cov zaub mov yog tsim nyog txhawm rau txo qis kev ntxhov siab ntawm lub txiav, kom nws rov zoo.

Nws yog qhov yuav tsum tau cais tawm ntawm cov ntawv qhia zaub mov:

  • fried, greasy and smoked foods;
  • buffet;
  • ice cream;
  • khoom noj kaus poom;
  • nceb;
  • marinades;
  • nqaij thiab ntses rog;
  • pickles;
  • tshuaj yej thiab kas fes;
  • cawv thiab carbonated haus.

daim ntawv teev npe no tuaj yeem nthuav dav los ntawm koj tus kws kho mob. Nws kuj tseem ua cov ntawv qhia zaub mov zaum kawg, suav nrog tus yam ntxwv ntawm tus neeg mob txoj kev noj qab haus huv.

Txhais tau

Kev tsis quav ntsej txog qhov tsis txaus enzyme ua rau muaj kev txhim kho ntawm txhua yam teeb meem. Ua ntej ntawm tag nrho cov, ib tug neeg yuav pheej yws yws txog qhov tsis xis nyob. Kev sib koom ua ke ntawm tus kab mob yog xeev siab thiab ntuav ntuav. Nyob rau tib lub sijhawm, kev ua haujlwm ntawm lub plab zom mov yuav tsis zoo. Raws li qhov tshwm sim: poob qab los noj mov, poob phaus, raws plab, mob tas likev xav, flatulence, tsam plab, belching.

Tawm tsam keeb kwm yav dhau los ntawm kev tsis txaus enzymatic, intoxication ntawm cov kab mob ntawm cov kab mob ntev tshwm sim. Raws li qhov tshwm sim, kev ua haujlwm ntawm cov hlab plawv system cuam tshuam rau tus neeg, qhov xwm txheej ntawm daim tawv nqaij zuj zus, qib ntawm lub cev muaj zog txo qis, cov kab mob hauv lub paj hlwb thiab endocrine tshwm sim.

Nws yog ib qho tseem ceeb kom nco ntsoov tias qhov tsis muaj enzyme tsis muaj kev ywj pheej. Nws yeej ib txwm muaj cov tsos mob ntawm qee yam kab mob. Tsis quav ntsej tus kab mob ua rau lub fact tias lub hauv paus pathology nce. Raws li qhov tshwm sim, kev hem thawj tsim tsis yog rau kev noj qab haus huv nkaus xwb, tab sis kuj rau lub neej ntawm tus neeg mob.

Cov tsos mob ntawm tus kab mob
Cov tsos mob ntawm tus kab mob

Kev Tiv Thaiv

Txhawm rau tiv thaiv tus kab mob, nws txaus los kho txhua yam kab mob hauv lub sijhawm thiab npaj cov zaub mov kom raug. Kev noj ntau dhau yuav tsum zam. Tsis tas li ntawd, koj yuav tsum tau hloov kho cov khoom noj. Nws raug nquahu kom ua raws li cov hauv paus ntsiab lus ntawm kev noj zaub mov kom raug.

Cov neeg muaj enzyme deficiency xav tau tshuaj noj mus ib txhis. Txhawm rau zam qhov mob thiab ua kom tsis zoo ntawm kev noj qab haus huv, koj yuav tsum tso cov khoom noj uas muaj rog, kib thiab haus luam yeeb, nrog rau cov dej qab zib uas muaj carbonated thiab cawv.

Nyob hauv kaw

Enzymatic deficiency yog ib yam kab mob pathological uas cov enzymes tsim tawm tsis sib haum rau qhov xav tau tiag tiag ntawm lub cev. Yog tias thawj qhov kev ceeb toom tshwm sim, koj yuav tsum hu rau tus kws kho mob lossis tus kws kho mob gastroenterologist. Tus kws kho mob yuav ua kev kuaj mobkev ntsuas thiab raws li lawv lub hauv paus yuav ua rau kev kho mob zoo tshaj plaws.

Pom zoo: