Cov tsos mob cuam tshuam nrog hemolytic uremic syndrome thiab nws txoj kev kho mob

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Cov tsos mob cuam tshuam nrog hemolytic uremic syndrome thiab nws txoj kev kho mob
Cov tsos mob cuam tshuam nrog hemolytic uremic syndrome thiab nws txoj kev kho mob

Video: Cov tsos mob cuam tshuam nrog hemolytic uremic syndrome thiab nws txoj kev kho mob

Video: Cov tsos mob cuam tshuam nrog hemolytic uremic syndrome thiab nws txoj kev kho mob
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Anonim

Yog li koj yuav tsum paub ua ntej ntawm kev sib txuas nrog hemolytic uremic syndrome (HUS luv luv). Cov kws kho mob koom nrog tus kab mob no feem ntau nrog peb cov tsos mob: mob raum tsis ua haujlwm, hemolytic anemia, thiab thrombocytopenia. Nws yuav tsum tau muab sau tseg hais tias lub xeem kos npe rau feem ntau yog lub feem ntau pronounced. Tus kab mob no feem ntau kuaj tau rau cov menyuam yaus.

hemolytic uremic syndrome
hemolytic uremic syndrome

Yuav ua li cas

Lub ntsiab tseem ceeb uas cuam tshuam nrog hemolytic uremic syndrome yog kev tsis haum tshuaj rau cov tshuaj, nrog rau kev kis tus kab mob. Yog li ntawd, nws yog ib qho tseem ceeb uas tus kab mob pib tshwm sim tom qab mob ua pa thiab plab hnyuv los yog thaum noj tshuaj tua kab mob. Hais txog lub pathogenesis ntawm HUS, nyob rau hauv no hais txog, qhov tseem ceeb tshaj plaws yog txuas nrog lub xub ntiag ntawm autoallergic cov tshuaj tiv thaiv. Qee zaum, lawv tuaj yeem ua rau mob microangiopathy.

hemolytic uremic syndrome nyob rau hauv cov me nyuam
hemolytic uremic syndrome nyob rau hauv cov me nyuam

Symptomatics

Cov cim qhia dab tsi feem ntau tshwm sim los ntawm hemolytic uremic syndrome? Nws yuav tsum tau muab sau tseg tias cov chav kawm ntawm tus kab mobconditionally muab faib los ntawm kws kho mob ua peb lub sij hawm. Thawj, prodromal, tuaj yeem kav ib hnub mus rau ob lub lis piam. Qhov thib ob, lub thiaj li hu ua "lub sij hawm ncov" - los ntawm ib mus rau peb lub lis piam. Tom qab ntawd los txog lub sijhawm rov qab los (lossis tuag) ntawm tus neeg mob.

thawj feem ntawm tus kab mob feem ntau zoo li lom thiab nrog cov tsos mob xws li ntuav, mob plab, raws plab, nrog rau cov ntshav. Qee cov neeg mob nyob rau theem no muaj convulsions, tsaug zog thiab txawm tias tsis nco qab. Tom qab lub sij hawm prodromal, ntau tus neeg mob tau pom qhov rov zoo. Cov kws kho mob tshwj xeeb kuj koom nrog hemolytic anemia, thrombocytopenia thiab lub raum puas nrog hemolytic-uremic syndrome. Cov kws kho mob nco ntsoov tias daim duab kho mob, raws li txoj cai, yog qhov txawv ntawm polymorphism. Hauv qee tus neeg mob, qhov tshwm sim ntawm qhov teeb meem hemolytic tuaj yeem tswj hwm, hauv lwm tus - cov tsos mob ntawm lub raum tsis ua haujlwm. Hemolytic anemia yog suav tias yog ib qho mob tshwm sim rau txhua tus neeg mob - nws tshwm nyob rau hauv nruab nrab ntawm HUS.

Hemolytic-uremic syndrome nyob rau hauv cov menyuam yaus ntawm theem ob yog tus cwj pwm los ntawm kev tuag ntawm daim tawv nqaij. Nyob rau hauv lub xub ntiag ntawm jaundice, hyperbilirubinemia yuav raug kuaj pom. Cov tshuaj tiv thaiv Direct Coombs feem ntau yog qhov tsis zoo, hemoglobin txo qis, tus lej ntawm erythrocytes raug txo. Tsis tas li, cov neeg mob feem ntau muaj qhov ntswg.

Kev kho mob hemolytic uremic syndrome
Kev kho mob hemolytic uremic syndrome

Diagnosis

Feem ntau, cov kws kho mob kuaj HUS raws li peb lub ntsiab lus tseem ceeb: muaj hemolytic anemia, thrombocytopenic purpura, thiab uremia. Feem ntau, daim duab kho mob zoo li Moszkowitz's syndrome.(kev puas tsuaj rau lub raum, ntshav txhaws, thiab lwm yam), nrog rau qhov sib txawv ntawm qhov tom kawg no feem ntau pom hauv cov menyuam yaus, thiab microthrombosis feem ntau tshwm sim hauv plawv thiab daim siab.

Hemolytic-uremic syndrome: kev kho mob

Kev Tiv Thaiv Kev Tawm Tsam Tawm Tsam yog lub hom phiaj tseem ceeb ntawm kev kho mob. Raws li txoj cai, cov kws kho mob qhia tag nrho lawv cov kev siv zog los tiv thaiv intravascular coagulation. Heparin thiab prednisolone pab tau zoo. Yog tias kev kho mob ua tsis tiav, hemodialysis raug qhia.

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