Pseudomyxoma ntawm peritoneum: ua rau, tsos mob, kuaj mob thiab kho

Cov txheej txheem:

Pseudomyxoma ntawm peritoneum: ua rau, tsos mob, kuaj mob thiab kho
Pseudomyxoma ntawm peritoneum: ua rau, tsos mob, kuaj mob thiab kho

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Video: Pseudomyxoma ntawm peritoneum: ua rau, tsos mob, kuaj mob thiab kho
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Pseudomyxoma ntawm peritoneum yog ib yam kab mob uas tshwm sim los ntawm kev sib sau ntawm cov hnoos qeev uas rov tsim dua lub sijhawm.

peritoneal pseudomyxoma cov cim theem kawg
peritoneal pseudomyxoma cov cim theem kawg

txhais li cas?

Lub sijhawm tau hais los ntawm tus kws tshawb fawb Werth hauv xyoo 1884. Nws yog Ameslikas siv rau cov neeg mob ntawm cov mob theem nrab provoked los ntawm cyst rupture. Sij hawm dhau mus, nws tuaj yeem pom tau tias pseudomyxoma ntawm lub peritoneum ua rau kev txav ntawm cov tshuaj nyob rau hauv lub appendix rau hauv cov kab noj hniav, uas, nyob rau hauv lem, provokes ib tug breakthrough nyob rau hauv cov zis los yog bile.

Cov kws tshawb fawb tau pom tias cov hnoos qeev tuaj yeem tshwm sim vim qhov tshwm sim ntawm qhov tshwm sim vim yog kev ncab ntawm phab ntsa ntau dhau los yog txo qis hauv nws cov tuab, nrog rau thaum lub sijhawm phais: tshem tawm cov cyst lossis daim ntawv ntxiv.

Thiab nyob rau hauv lub tshuab nqus tsev?

Thaum tshuaj xyuas cov kab noj hniav ntawm qhov loj, nws tuaj yeem pom tau tias pseudomyxoma ntawm lub peritoneum tau ntim nrog cov tshuaj serous, uas cov hnoos qeev sib xyaw. Qhov no pib o, vim yog qhov deformation ntawm phab ntsa tshwm sim:

  • thickening;
  • dej;
  • ntxhi.

Qee zaum, qhov chaw hloov mus ua velvet zoo li, thaum nyob hauvhemorrhages tshwm sim hauv qee qhov chaw. Nrog rau txoj kev loj hlob ntawm pathology, lub plab hnyuv loops, omentum thiab plab yog soldered. Cov khoom nruab nrog cev poob qhov kev txav mus los uas tsim nyog rau kev ua haujlwm ib txwm muaj.

peritoneal pseudomyxoma prognosis
peritoneal pseudomyxoma prognosis

Kawm txog thaj chaw puas nyob rau hauv lub tshuab kuaj kab mob, koj tuaj yeem pom tias hauv cov hlwb uas cov hnoos qeev nyob, muaj cov txheej txheem ntawm cov ntaub so ntswg, uas suav nrog cov infiltrate. Lub epithelium nyob rau hauv xws li hloov hlwb yog:

  • cub;
  • paj.

Cov kab mob ntawm cov kab mob hloov pauv raws sijhawm, qhov no yog txiav txim los ntawm theem ntawm pathology. Nrog rau kev kuaj mob ntawm "pseudomyxoma ntawm peritoneum", cov hlwb tshwm sim hauv cov hnoos qeev:

  • lymphocytes;
  • fibroblasts;
  • multi-core giants;
  • Ypolymorphic leukocytes;
  • histocytes;
  • kab mob epithelium.

Cov tom kawg tuaj yeem cog rau hauv peritoneum. Nws nkag mus rau hauv lub cev los ntawm ib tug perforation. Nws yog vim qhov kev loj hlob ntawm cov epithelium uas peritoneal pseudomyxoma raug cais raws li tus kab mob neoplastic, cov tsos mob uas feem ntau tsis pom tseeb. Cov txheej txheem yog sluggish, txhawb los ntawm hnoos qeev, suav hais tias yog inflammatory.

Ib kab mob txaus ntshai?

Cov qog ntawm peritoneum muaj ob hom:

  • primary;
  • secondary.

Los ntawm cov tshuaj malignant feem ntau captures precisely metastatic, uas yog, theem nrab. Raws li rau cov thawj, cov pseudomyxoma ntawm lub peritoneum kuj belongs rau lawv. Cov tsos mob ntawm tus kab mob thaum xub thawj yog kiag li tsis pom. Nrog kev loj hlob ntawm pathologycov hlwb kis mus rau saum npoo ntawm peritoneum yam tsis muaj kev cuam tshuam rau cov kabmob uas nyob sib ze. Qhov no yog ib qho tseem ceeb ntawm kev mob qog noj ntshav tau piav qhia. Txoj kev faib cov kab mob kis tau yog diffuse.

Nyob rau hauv qhov xwm txheej uas, ntxiv rau omentum, lwm cov ntaub so ntswg kuj raug cuam tshuam, lawv hais tias peritoneal pseudomyxoma raug kuaj pom, qhov kev cia siab ntawm qhov poob siab. Qhov no feem ntau yog vim qhov tseeb tias cov kab mob feem ntau pom tawm tsam keeb kwm yav dhau los ntawm cov kab mob oncological hauv lwm lub cev.

Kev kuaj mob ntawm pseudomyxoma peritoneum
Kev kuaj mob ntawm pseudomyxoma peritoneum

Diagnosis

Pseudomyxoma peritoneum feem ntau yog kuaj los ntawm laparotomy. Nws raug sau tseg rau cov tsos mob hauv qab no:

  • mob plab (feem ntau dull);
  • plab o kom tsis muaj laj thawj.

Qhov no tshwm sim vim muaj cov kua dej ntau hauv cov ntaub so ntswg ntawm lub cev.

Highlight:

  • limited swb;
  • pseudomyxoglobulosis.

Qhov no tshwm sim li cas?

Raws li txoj cai, tus kab mob tshwm sim nws tus kheej tawm tsam keeb kwm ntawm lub cyst ruptured. Qhov no yog vim qhov tseeb tias qhov kev tawg ua rau nkag mus rau hauv lub plab kab noj hniav tsis yog tsuas yog cov hnoos qeev, tab sis kuj ntawm cov epithelium. Nws cov hlwb muaj lub peev xwm tshwj xeeb los cog lawv tus kheej rau hauv cov ntaub so ntswg uas lawv tsaws rau. Thaum lub sij hawm, cov chaw reborn kuj pib tsim cov hnoos qeev.

Raws li txoj cai, kev kuaj mob ntawm "peritoneal pseudomyxoma" txhais tau hais tias tus kab mob yog malignant. Pathology yog superficial, tsis ua rau muaj kev cuam tshuam ntawm kev ua haujlwm ntawm lub cev thiab lub cev. Pseudomyxoma yog mobile, nws yog tus cwj pwm los ntawm "tus kab mobtuav." Niaj hnub no, tib txoj kev zoo rau kev kuaj mob yog kev phais, thaum lub sijhawm kuaj cov ntaub so ntswg tau txais. Kev lees paub ntawm pathology yog muab los ntawm biopsy.

Kev kho mob pseudomyxoma peritoneum
Kev kho mob pseudomyxoma peritoneum

Yuav ua li cas?

Yuav tsum tau npaj rau qhov tseeb tias thaum kuaj xyuas "pseudomyxoma ntawm peritoneum", kev kho mob yog phais. Tsis muaj lwm txoj hauv kev zoo los daws cov kab mob pathology tseem tau tsim. Yog hais tias qhov kev loj hlob yog benign, nws yuav tsum tau excised, txiav txim siab qhov twg cov ntaub so ntswg tseem noj qab nyob zoo.

Thaum tus kab mob degenerates mus rau hauv ib tug malignant, tsuas yog cov neeg uas npaj mus rau ib tug radical tshem tawm tau muaj txoj hauv kev rau kho. Nyob rau hauv cov ntaub ntawv no, prognosis yog unfavorable. Kev rov ua tiav tiav tuaj yeem xav tau nyob rau hauv rooj plaub ntawm cov txheej txheem qog nqaij hlav, tab sis tom qab kev yug me nyuam, txawm tias kev phais tsis tuaj yeem cuam tshuam tag nrho cov txheej txheem ntawm kev tsim khoom thiab sib sau cov hnoos qeev.

Tsis yog ib tus kws kho mob tuaj yeem txiav txim siab seb qhov mob puas tau tshwm sim lawm. Qhov no tau kuaj pom thaum kuaj histological, uas yuav qhia tau tias tsis muaj cov qog nqaij hlav qog nqaij hlav hauv cov ntaub so ntswg coj mus kuaj, tab sis tsis tuaj yeem lav tias lawv tsis nyob hauv lub cev txhua.

Thaum kuaj pom "pseudomyxoma ntawm lub peritoneum", kev kho mob raug xaiv, xav tias cov qog tau dhau los ua malignancy. Qhov no yog vim muaj ntau zaus ntawm relapses, invasions.

pseudomyxoma peritoneum cov tsos mob
pseudomyxoma peritoneum cov tsos mob

Yuav ua li cas?

Ua ntej koj paub tias dab tsi yog cov cim qhia ntawm pathology hauv kev kuaj mob ntawm "pseudomyxoma ntawm peritoneum" (theem kawg),ua ntej koj yuav tsum tau qhia meej, kev kho hluav taws xob thiab tshuaj kho mob tau pom tias tsis muaj txiaj ntsig hauv kev tawm tsam tus kabmob.

Tam sim no, tsis muaj kev kho mob tshwj xeeb rau tus kab mob no. Qhov yooj yim tshem tawm cov hnoos qeev tau ua pov thawj tias tsis muaj txiaj ntsig, txij li cov hlwb uas tau nkag mus rau hauv epithelium txuas ntxiv tsim nws.

Nws ntseeg tau tias cov txiaj ntsig zoo tuaj yeem ua tiav nrog kev kho hluav taws xob thaum cov ntaub so ntswg cuam tshuam tau irradiated nrog platinum, kub isotopes.

Yog tsis muaj kev kho mob kom raug, tus neeg mob tuag hauv ib mus rau ob xyoos. Qee zaum, cov kab mob kis tau nrog cov tsos ntawm fistulas ntawm daim tawv nqaij.

peritoneal pseudomyxoma
peritoneal pseudomyxoma

tseem ceeb nuances

Kev txheeb cais hais tias pseudomyxoma ntawm peritoneum tshwm sim nyob rau hauv kwv yees li 1% ntawm cov neeg mob, yog li nws raug cais raws li qhov tsawg kawg nkaus. Nws qhov kev phom sij yog nyob rau hauv cov chav kawm latent, kev loj hlob atypical thiab tsis pom kev zoo.

Qee qhov xwm txheej, kev txhim kho ntawm pathology tshwm sim tawm tsam keeb kwm ntawm appendicular mucin. Ntawm cov tsos mob uas ua rau nws muaj peev xwm xav tias oncology yog plab hnyuv.

hom mucin hauv qab no yog yam ntxwv ntawm tus kab mob:

  • Free.
  • tso nyiaj. Paub qhov txawv ntawm qhov loj thiab me. Lawv haum nruj heev rau qhov chaw peritoneal. Nyob rau hauv lub deposits, inflammatory txheej txheem tshwm sim thiab mesothelial hlwb. Qee zaum, fibroblasts thiab capillaries muaj nyob ntawm no. Tab sis cov hlwb uas tsis yog yas feem ntau tsis tuaj yeem kuaj pom.
  • pas. Cov pawg no feem ntau muaj cov ntaub so ntswg collagenized raws li lawv lub plhaub. Hauv sciencecov formations no hu ua cais mucin.

Leej twg ntseeg?

Nyob rau xyoo tas los no, ntau lub tsev kho mob Israeli tau tshwm sim uas tau lees tias muaj kev kho mob qog noj ntshav tag. Raws li txoj cai, cov koom haum zoo li no tsis ua raws li cov lus cog tseg, tab sis ua kev tshaj tawm tsis txaus ntseeg, txhawb kev cia siab rau cov neeg mob thiab lawv cov txheeb ze.

peritoneal pseudomyxoma
peritoneal pseudomyxoma

Nco ntsoov tias yuav tsum xaiv cov tsev kho mob tom qab ua tib zoo kawm cov ntaub ntawv, nrog rau cov kev tshuaj xyuas ntawm cov neeg tau txais kev kho mob tiag tiag. Ua tib zoo saib xyuas cov kws kho mob tsis zoo thiab cov kev pabcuam tsis zoo.

Pom zoo: