Hepatolienal Syndrome: Cov tsos mob, kev kho mob

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Hepatolienal Syndrome: Cov tsos mob, kev kho mob
Hepatolienal Syndrome: Cov tsos mob, kev kho mob

Video: Hepatolienal Syndrome: Cov tsos mob, kev kho mob

Video: Hepatolienal Syndrome: Cov tsos mob, kev kho mob
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"Syndrome" hauv Greek txhais tau tias "kev sib sau" lossis "kev sib txuas". Nyob rau hauv cov tshuaj, qhov no characterization yog muab rau cov kab mob uas muaj ib tug xov tooj ntawm recognizable nta, feem ntau tshwm sim ua ke. Yog li, cov tsos mob tshwm sim ua ntej qhov kev kuaj pom tseeb tuaj yeem raug hu ua tus mob syndrome. Ib yam mob no yog hepatolienal syndrome.

yam ntxwv

Hepato-splenic syndrome yog lub npe thib ob rau tus mob no. Nws yog tus cwj pwm los ntawm kev nce hauv daim siab thiab tus po, ntsig txog, kev ua haujlwm ntawm cov kabmob no cuam tshuam. Hepatolienal syndrome tshwm sim nyob rau hauv cov kab mob ntev ntawm cov kab mob hepatobiliary thiab cov ntshav ncig hauv "portal vein - splenic vein" system.

Venous ncig hauv daim siab thiab tus po muab kev piav qhia txog seb cov kabmob no txuas nrog li cas thiab lawv cuam tshuam rau ib leeg hauv kev sib txawv xws li hepatolienal syndrome. Koj tuaj yeem taug qab qhov kev sib txuas ntawm venous ntawm cov kabmob no.

hepatolienal syndrome
hepatolienal syndrome

Cov hlab ntsha tseem ceeb yog cov hlab ntsha portal. Nws sau cov ntshav los ntawmspleen thiab lwm yam kabmob plab. Tom qab ntawd nws nkag mus rau hauv daim siab, qhov chaw uas nws tshem tawm cov co toxins uas tsis zoo thiab tom qab ntawd faib cov as-ham thoob plaws hauv lub cev. Ib feem ntawm cov hlab ntsha portal yog splenic, yog li tus po yog nyob rau hauv kev sib raug zoo nrog lub siab thiab cov txheej txheem tshwm sim hauv nws. Qhov no piav qhia yog vim li cas lub siab thiab tus po yog cuam tshuam rau hauv hepatolienal syndrome.

YPathogeny ntawm hepatolienal syndrome

Cov ntshav tsis txaus tuaj yeem tshwm sim vim qhov nqaim ntawm lumen ntawm cov hlab ntsha portal. Muaj stagnation ntawm cov ntshav thiab, yog li ntawd, nce ntshav siab. Vim li cas qhov no tshwm sim? Nov yog qee qhov laj thawj:

Sab nraud compression ntawm lub portal leeg. Qhov no tuaj yeem tshwm sim hauv daim siab thiab ntawm lub hepatoduodenal ligament ntawm nkag mus rau hauv lub cev. Hauv qhov no, nws tuaj yeem soj ntsuam cov tsos mob ntawm tus mob hepatolienal nrog cov kab mob xws li:

  • Cirrhosis ntawm daim siab.
  • mob siab mob siab.
  • Thrombosis ntawm cov hlab ntsha portal thiab cov hlab ntsha loj nyob ib sab.
  • Primary daim siab mob.
  • Kev mob plawv ntawm sab xis ib nrab ntawm lub siab.
  • kab mob ducts, qog thiab cysts.
  • Hepatic vein thrombosis.

2. Narrowing ntawm lumen ntawm cov leeg:

  • Thrombosis ntawm cov hlab ntsha portal thiab nws cov ceg loj.
  • Hepatic vein thrombosis, lossis Budd-Chiari Syndrome.
pathogenesis ntawm hepatolienal syndrome
pathogenesis ntawm hepatolienal syndrome

Ntxiv rau qhov ua rau muaj kev puas tsuaj uas tuaj yeem ua rau lub siab thiab tus po, qhov no tuaj yeem tshwm sim raws li kev tiv thaiv ntawm lub cev rau cov kab mob.

Stages

Muaj ntau theem ntawm hepatolienal syndrome:

  1. Thawj theem tuaj yeem siv sijhawm ntau xyoo. Cov kev mob dav dav yog txaus siab, mob ntshav qab zib tsawg, leukopenia thiab neutropenia raug pom. Lub siab tsis loj, tab sis tus po mas loj dua.
  2. theem thib ob yog tus cwj pwm los ntawm kev nce siab hauv daim siab. Muaj cov cim qhia txog kev ua txhaum ntawm nws txoj haujlwm. Tej zaum yuav kav ntau lub hlis.
  3. Thib peb. Nws lub sijhawm yog kwv yees li ib xyoos. Qhov txo qis thiab thickening ntawm daim siab yog yam ntxwv, anemia nce, cov tsos mob ntawm kub siab, ascites, gastrointestinal los ntshav, thiab esophageal varicose veins tshwm..
  4. theem plaub. Tus cwj pwm los ntawm kev tsis txaus ntseeg, o thiab cov tsos mob ntawm los ntshav.

Kev tshwm sim

Hepatolienal Syndrome feem ntau tshwm sim rau cov menyuam yaus.

Cov menyuam yaus thiab cov neeg laus tuaj yeem muaj qhov sib txawv:

  • kab mob sib kis.
  • kab mob sib kis.
  • Congenital hemolytic anemia.
  • Congenital thiab kis kab mob ntawm cov hlab ntsha portal, spleen.
  • Hemolytic disease in the newborn.
  • Kev haus dej haus cawv.
  • Hepatolienal Syndrome diagnostic kev kuaj mob
    Hepatolienal Syndrome diagnostic kev kuaj mob

pab pawg pheej hmoo thiab lawv cov tsos mob

Txhua yam kab mob uas tuaj yeem ua rau mob siab hepatolienal tuaj yeem muab faib ua pawg:

  1. Kab mob siab thiab mob ntev. Cov pab pawg no yog tus cwj pwm los ntawm qhov mob lossis kev xav hnyav hauv txoj cai hypochondrium,dyspeptic mob, pruritus, jaundice. Ua rau muaj xws li kab mob siab yav dhau los, kev sib cuag nrog cov neeg mob kis, raug mob lossis phais, haus dej cawv ntev, noj tshuaj hepatotoxic, mob plab yav dhau los, kub taub hau.
  2. Kev kuaj mob sib txawv ntawm hepatomegaly thiab hepatolienal syndrome
    Kev kuaj mob sib txawv ntawm hepatomegaly thiab hepatolienal syndrome
  3. Cov kab mob cia. Lawv pom nyob rau hauv tib tsev neeg lossis cov txheeb ze ze.
  4. Kab mob kis kab mob thiab kab mob cab. Nrog rau kev ua kom qaug zog, ua npaws, mob caj dab thiab myalgia.
  5. Kab mob ntawm cov hlab plawv. Lawv nrog tachycardia, kab mob plawv ischemic, tsub zuj zuj ntawm cov kua dej nyob rau hauv lub pericardial kab noj hniav, o thiab hloov nyob rau hauv lub configuration ntawm lub plawv.
  6. Kab mob ntawm cov ntshav thiab lymphoid cov ntaub so ntswg. Cov pab pawg no muaj cov tsos mob xws li qaug zog, ua npaws, mob qog nqaij hlav.

Symptomatics

Yog tus neeg mob muaj tus mob hepatolienal, cov tsos mob yuav ua raws li hauv qab no:

  1. Ua kom lub siab thiab tus po. Mob ntawm palpation.
  2. poob phaus.
  3. Kev ua haujlwm ntawm cov qog endocrine cuam tshuam.
  4. Teeb meem hauv plab hnyuv.
  5. Npaj. Paleness thiab dryness ntawm daim tawv nqaij.
  6. Muaj peev xwm ua kua dej hauv plab.
  7. Cov tsos mob ntawm tus mob hepatolienal syndrome
    Cov tsos mob ntawm tus mob hepatolienal syndrome
  8. mob leeg thiab pob qij txha.
  9. Yellowing of whites of ob lub qhov muag.
  10. Tachycardia, ua tsis taus pa.
  11. Ntxhaisrau tes, plaub hau poob.

Txhawm rau kuaj mob, nws yog qhov yuav tsum tau kuaj xyuas, thiab txhawm rau txhawm rau txheeb xyuas cov kab mob ntau ntxiv, kev kuaj mob.

Diagnosis

Yog tias cov tsos mob saum toj no tshwm sim, kev kuaj mob sib txawv ntawm hepatomegaly thiab hepatolienal syndrome tau ua tiav. Txhawm rau ua qhov no, nws yog qhov yuav tsum tau siv tag nrho cov kev ntsuas. Ib qho ntawm thawj cov ntsiab lus yog kev kuaj ntshav dav dav thiab nws txoj kev tshawb fawb biochemical. Txhawm rau tsim kom muaj qhov ua rau hepatolienal syndrome, kev kuaj mob sib txawv tsuas yog tsim nyog. Hauv nws lub moj khaum:

  • Echography ntawm daim siab thiab spleen, gallbladder, plab hlab ntsha.
  • Computed tomography.
  • daim siab thiab spleen scan.
  • X-ray ntawm duodenum.
  • Laparoscopy.
  • Puncture biopsy ntawm daim siab thiab spleen.
  • Kev kuaj mob pob txha thiab cov qog ntshav.
  • Hepatolienal Syndrome diagnostic kev kuaj mob
    Hepatolienal Syndrome diagnostic kev kuaj mob

Tam sim no, kev tshawb fawb tsis nyob twj ywm thiab kev tshuaj xyuas ntawm cov kabmob yog txuas ntxiv nthuav dav hauv kev kuaj mob xws li hepatolienal syndrome. Kev kuaj mob sib txawv ntawm tus kab mob hauv qab, suav nrog cov duab kho mob thiab lub xeev ntawm daim siab, yog tias muaj, yog lub luag haujlwm tseem ceeb.

Kev kho mob thiab teeb meem ntawm tus kab mob

Raws li txoj cai, kev kho mob rau hepatolienal syndrome muaj nyob rau hauv kev txheeb xyuas cov txheej txheem pathological thiab kho nws. Nws tsis yog ib qho kab mob ywj pheej. Yog tias koj tau kuaj pom"hepatolienal syndrome", kev kho mob yuav tsum tau ua los ntawm tus kws kho mob gastroenterologist. Hauv qhov no, hepatoprotectors, tshuaj tua kab mob, tshuaj hormones thiab vitamins yog siv. Nyob rau hauv txhua rooj plaub, yuav tsum muaj ib tug neeg mus kom ze, coj mus rau hauv tus account lub etiology ntawm tus kab mob.

Kev kho mob hepatolienal syndrome
Kev kho mob hepatolienal syndrome

Yog tias koj nco tus kab mob thiab tsis kho, qhov kev tshwm sim tuaj yeem ua rau poob siab. Cov teeb meem ntawm tus mob no yog cirrhosis ntawm daim siab, thrombosis ntawm cov hlab ntsha ntawm lub siab, o ntawm lub gallbladder, kab mob ntshav. Hauv cov xwm txheej zoo li no, kev tshem tawm ntu ntawm daim siab thiab tus po, lossis kev hloov pauv hauv nruab nrog cev thiab hloov ntshav.

Thaum thawj theem, cov neeg mob tuaj yeem ua haujlwm thiab tuaj yeem tiv taus kev tawm dag zog me ntsis. Nyob rau yav tom ntej, yog tias qhov xwm txheej hnyav zuj zus, tus neeg mob yuav xiam oob qhab.

Kev Tiv Thaiv

Yuav kom tsis txhob nco qhov pib ntawm kev txhim kho pathology, koj yuav tsum:

  • Mus kuaj ntshav thiab tso zis tsis tu ncua.
  • Tau tshuaj ntsuam raws sijhawm, tshwj xeeb yog tias koj muaj kev pheej hmoo.
  • Tiv thaiv kab mob siab hepatolienal feem ntau suav nrog kev tawm tsam cov kab mob ntawm daim siab thiab tus po.
  • Nws yog qhov yuav tsum tau ua raws li kev noj zaub mov kom zoo kom cov zaub mov muaj cov rog, cov protein thiab carbohydrates thiab, ntawm chav kawm, vitamins.
  • Tsis txhob haus cawv, haus luam yeeb thiab coj txoj kev noj qab haus huv.

Tsis muaj kab mob tsis zoo, thiab tshwj xeeb tshaj yog tias lawv txhawj xeeb txog cov kabmob tseem ceeb xws li daim siab thiab tus po. Kev tshawb nrhiav cov teeb meem raws sij hawm, thiab tom qab ntawd txausCov kev kho mob muaj peev xwm ua tau zoo.

Pom zoo: