Löfgren's syndrome: ua rau, chaw kho mob, kho, tiv thaiv

Cov txheej txheem:

Löfgren's syndrome: ua rau, chaw kho mob, kho, tiv thaiv
Löfgren's syndrome: ua rau, chaw kho mob, kho, tiv thaiv

Video: Löfgren's syndrome: ua rau, chaw kho mob, kho, tiv thaiv

Video: Löfgren's syndrome: ua rau, chaw kho mob, kho, tiv thaiv
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Kab mob kab mob ib txwm ua tsis meej rau lub ntiaj teb kev kho mob. Ib tug ntawm lawv yog sarcoidosis, uas tsis muaj kev cuam tshuam etiology, tab sis manifests nws tus kheej nyob rau hauv daim ntawv ntawm o ntawm connective cov ntaub so ntswg nyob rau hauv ntau yam kabmob thiab cov ntaub so ntswg nrog tsim granulomas. Löfgren's syndrome yog ib qho tshwj xeeb ntawm sarcoidosis cuam tshuam rau ntawm daim tawv nqaij, cov qog nqaij hlav hauv lub cev, thiab cov pob qij txha.

Vim txoj kev loj hlob

Tus kab mob yog raws li kev txhim kho ntawm cov tshuaj tiv thaiv autoimmune. Lub cev tiv thaiv kab mob tsis ua haujlwm, thiab cov qe ntshav dawb pib tua cov hlwb noj qab haus huv hauv lub ntsws, pob qij txha, thiab tawv nqaij.

Löfgren's Syndrome
Löfgren's Syndrome

Löfgren's syndrome feem ntau tshwm sim hauv cov poj niam hluas (20-35 xyoo). Cov menyuam yaus feem ntau tsis mob. Löfgren's syndrome pib mob heev, thiab tom qab ntawd maj mam cov kev kho mob tshwm sim yuav ploj mus ntawm lawv tus kheej. Feem ntau muaj cov kab mob zoo.

Ntxiv rau qhov kev xav ntawm kab mob thiab kab mob ntawm txoj kev loj hlob ntawm sarcoidosis, tseem muaj kev xav tias tus kab mob no tshwm sim hauv cov neeg uas muaj kev sib cuag mus ntev nrog cov tshuaj volatile hauv cov chaw tsim khoom. Tsis txhob plam qhov pom ntawm qhov tshwm sim ntawm keeb kwm. Yog li ntawd, sarcoidosis yog polyetiological autoimmune kab mob.kab mob.

Kev kho mob tshwm sim

Löfgren's syndrome hauv sarcoidosis manifests nws tus kheej polysymptomatically. Clinical manifestations pib mob heev. Ib tug neeg tsim erythema nodosum ntawm lub cev, nws zoo li kis mus rau ceg, nraub qaum, plab, caj dab. Cov nodes yog oval nyob rau hauv cov duab, lawv txoj kab uas hla tuaj yeem ncav cuag 6 centimeters. Nws yog tsim nyog sau cia tias necrosis tsis tshwm sim ntawm qhov chaw ntawm erythema tsim.

Qhov tshwm sim tseem ceeb yog qhov swb ntawm cov qog ntshav hauv lub ntsws thiab cov hlab ntsws. Qhov no yog qhov txaus ntshai heev rau tus neeg mob:

  • hnoos tshwm;
  • qee zaus nce lub cev kub;
  • xav phem;
  • hmo ntuj tawm hws tshwm sim;
  • deteriorating pw tsaug zog;
  • poob ceeb thawj tshwm sim;

Tom qab Löfgren's syndrome yog tus cwj pwm los ntawm kev puas tsuaj ntawm kev sib koom tes. Lawv ua o, mob, thiab kev txav mus los zuj zus. Lub hom phiaj, nws tuaj yeem pom qhov nce hauv cov qog nqaij hlav ntawm lub caj dab, nrog rau hauv caj dab.

Löfgren's syndrome nyob rau hauv sarcoidosis manifests nws tus kheej
Löfgren's syndrome nyob rau hauv sarcoidosis manifests nws tus kheej

Yuav kuaj mob li cas?

Löfgren's syndrome yog tsim los ntawm kev kuaj mob thiab kuaj xyuas tus neeg mob los ntawm tus kws kho mob. Erythema nodosum yog qhov tseem ceeb hauv kev kuaj mob ntawm daim ntawv no ntawm sarcoidosis. Txawm li cas los xij, tus kws kho mob yuav tsum tau cais tus kab mob los ntawm tuberculosis lossis kab mob dermatovenereological.

Lab kuaj ntshav yuav qhia:

  • nce ESR;
  • leukocytosis;
  • gamma tsosglobulins.

Ntawm qhov x-ray, koj tuaj yeem pom tus yam ntxwv ntawm cov qog nqaij hlav, nrog rau cov pob txha pob txha. Qhov no yuav pab kom paub tseeb tias mob ntsws puas.

daim ntawv me me yuav tsum tau kuaj bronchoscopy nrog rau kev tsom xam biopsy. Thaum kuaj lub ntsws cov ntaub so ntswg, nws muaj peev xwm pom tus yam ntxwv histological qauv ntawm sarcoidosis: cov ntsiab lus ntawm ib tug epithelioid granuloma pom.

Kev kuaj mob lofgren syndrome
Kev kuaj mob lofgren syndrome

Kev Ntsuas thiab Teebmeem ntawm Kab Mob

Löfgren's syndrome tshwm sim ib tus zuj zus. Nws kav ntev npaum li cas thiab qhov kev kwv yees yog dab tsi, nws tuaj yeem teb tau tsuas yog raws li qee cov qauv. Nws paub tias tus neeg laus dua, qhov kev mob tshwm sim hnyav dua. Yog tias koj tsis mus ntsib kws kho mob raws sijhawm, tus mob yuav ncua sijhawm, thiab muaj teeb meem ntxiv rau nws:

  • bronchial obstruction;
  • ua pa tsis ua haujlwm;
  • kev txhim kho ntawm "cor pulmonale";
  • emphysema;
  • kab mob bacterial flora.

Ua pa tsis ua haujlwm tom qab broncho-obstruction. Tus neeg mob tus mob maj mam deteriorates raws li lub ntsws pib hloov los ntawm connective cov ntaub so ntswg, cov txheej txheem yuav tsum tsis txhob spontaneously tom qab 1-2 xyoos.

Maj mam, lub plawv pib nce vim tsis muaj oxygen hauv cov ntshav. Nrhiav kev kho mob, txawm li cas los xij, yuav tsum tsis txhob tsis quav ntsej, vim Löfgren's syndrome tam sim no kho tau.

lofgren's syndrome x-ray
lofgren's syndrome x-ray

Kev kho mob

Hmoov tsis zoo, cov kws kho mob tsis tuaj yeem kho sarcoidosis tag nrho,vim nws etiology tsis paub kiag li. Tab sis cov kws kho mob tau sau ib txoj kev kho tshwj xeeb uas tuaj yeem nres txoj kev txhim kho, tswj Lofgren's syndrome. Kev kho mob pib nrog kev teem caij ntawm steroidal anti-inflammatory tshuaj los txo kev tiv thaiv. Vitamin complexes, antioxidants, immunosuppressants kuj tau sau.

Cov kev kho mob yuav kav ntev li 8 lub hlis. Nws tag nrho yog nyob ntawm tus kheej yam ntxwv ntawm lub cev tiv thaiv kab mob. Kev soj ntsuam ntawm cov neeg mob los ntawm tus kws kho mob pulmonologist yog qhov yuav tsum tau ua, qhov zoo nws kav 5 xyoos.

Kev kho mob ntawm lofgren's syndrome
Kev kho mob ntawm lofgren's syndrome

Kev tiv thaiv dab tsi?

Txhawm rau tiv thaiv kev txhim kho ntawm sarcoidosis, ua ntej ntawm tag nrho, koj yuav tsum saib xyuas koj txoj kev ua neej. Khoom noj khoom haus yuav tsum sib npaug, muaj cov rog, proteins, carbohydrates nyob rau hauv kev pom zoo piv.

Cov neeg muaj kev pheej hmoo rau tus mob sarcoidosis yuav tsum tsis txhob haus luam yeeb, raug rau cov tshuaj hnyav.

Pom zoo: