Lymphatic-hypoplastic diathesis hauv cov menyuam yaus: cov tsos mob, ua rau, kev kho mob

Cov txheej txheem:

Lymphatic-hypoplastic diathesis hauv cov menyuam yaus: cov tsos mob, ua rau, kev kho mob
Lymphatic-hypoplastic diathesis hauv cov menyuam yaus: cov tsos mob, ua rau, kev kho mob

Video: Lymphatic-hypoplastic diathesis hauv cov menyuam yaus: cov tsos mob, ua rau, kev kho mob

Video: Lymphatic-hypoplastic diathesis hauv cov menyuam yaus: cov tsos mob, ua rau, kev kho mob
Video: Tshem tsis taus koj hauv kuv lub siab 3 (Daim Kawg) 2024, Lub Xya hli ntuj
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Lymphatic-hypoplastic diathesis hauv cov menyuam yaus yog ib qho teeb meem hauv lymphatic system, nrog rau hyperplasia (nce kev loj hlob) ntawm cov ntaub so ntswg lymphoid, kev ua haujlwm tsis zoo ntawm cov kab mob endocrine, kev hloov pauv hauv kev ua haujlwm thiab txo qis hauv kev tiv thaiv ntawm kev tiv thaiv kab mob. tus me nyuam lub cev.

Dab tsi ua rau

Hyperplasia ntawm cov hlwb ntawm cov kab mob lymphatic ua rau kev loj hlob ntawm thymomegaly - nce hauv thymus (los yog lwm lo lus, thymus), uas yog lub luag haujlwm rau lub xeev ntawm lub cev tiv thaiv kab mob thiab tsim cov tshuaj hormones.. Feem ntau, lub caj pas thymus yog tag nrho tsim nyob rau hauv thaum yau, thiab tom qab kov yeej cov hluas, cov txheej txheem rov qab pib tshwm sim hauv nws. Nrog rau txoj kev loj hlob ntawm thymomegaly hauv cov menyuam yaus, tsis yog tsuas yog kev nce hauv cov qog no hauv qhov loj, tab sis kuj nws txoj kev loj hlob rov qab qeeb, uas ua rau cov tsos mob ntawm kev tiv thaiv kab mob thiab kab mob endocrine.

Nws yuav zoo li tias qhov nce ntawm cov lymphocytes uas loj hlob hauv cov menyuam yaus nrog qhov tsis zoo ntawm txoj cai lij choj yuav tsum tsuas yog ntxiv dag zog rau nws txoj kev tiv thaiv thiab qhib.tiv thaiv reserves ntawm lub cev. Tab sis, hmoov tsis, qhov no tsis tshwm sim. Tus naj npawb ntawm lymphocytes hauv cov ntaub so ntswg lymphoid thiab ntshav tau nce sai heev, txawm li cas los xij, lawv tsis paub tab, uas txhais tau tias lawv tsis tuaj yeem ua tiav lawv lub hom phiaj tseem ceeb.

niam thiab me nyuam
niam thiab me nyuam

Kev tshwm sim

Tshuaj tseem tsis tau tsim qhov ua rau lymphatic-hypoplastic diathesis hauv cov menyuam yaus. Nws paub tias qhov no pathology feem ntau pom nyob rau hauv cov me nyuam tsis muaj zog thiab ntxov ntxov. Tsis tas li ntawd, nws ntseeg tau tias muaj cov kab mob endocrine mob ntev hauv niam kuj cuam tshuam rau kev tsim cov txheej txheem no.

Qhov kev pheej hmoo ntawm kev tsim cov kev tsis haum no (diathesis) yog txiav txim siab los ntawm cov chav kawm ntawm ntau yam pathologies hauv niam. Hauv qhov no, hais xws li:

  • kev ua haujlwm tsis txaus;
  • ua haujlwm nrawm;
  • fetal hypoxia;
  • birth trauma.

Cov xwm txheej ntawm tus menyuam mos thiab cov kab mob tam sim no tsis muaj qhov tseem ceeb.

Yuav ua li cas cov txheej txheem pathological tshwm sim

Lymphatic-hypoplastic diathesis hauv cov menyuam yaus yog tus cwj pwm los ntawm kev nce ntxiv thiab kev puas tsuaj rau adrenal cortex. Kev tsim ntawm hypocorticism provokes qhov txo qis hauv cov ntshav siab nrog rau cov leeg nqaij hypotension. Qhov no ua rau lub caj pas pituitary, uas ua rau muaj kev tsim cov tshuaj hormones ACTH thiab GH.

Lymphatic-hypoplastic diathesis hauv cov menyuam yaus ua rau txo qis hauv kev sib txuas ntawm catecholamines thiab glucocorticoids, uas pab tsim cov mineralocorticoids thiab theem nrab.hyperplasia ntawm lymphoid cov ntaub so ntswg thiab thymus suav nrog. Nrog rau qhov pathology no, cov menyuam yaus raug sau tseg:

  • tsis sib npaug ntawm dej-ntsev metabolism;
  • kev tsis txaus siab rau cov xwm txheej ntxhov siab;
  • nquag mob ntshav microcirculation;
  • siab permeability ntawm phab ntsa ntawm cov hlab ntsha ntawm cov hlab ntsha.

Vim li ntawd, toxicosis tsim, ua kom cov hnoos qeev hauv tsob ntoo bronchial thiab tsim cov mob hawb pob.

Lymphatic-hypoplastic diathesis hauv cov menyuam yaus yog tus cwj pwm los ntawm kev nce hauv thymus, nyuaj los ntawm kev hloov pauv hauv lub cev tsis muaj zog nrog kev tiv thaiv qis dua. Qhov no ua rau muaj qhov tshwm sim ntawm cov kab mob ua pa nyuaj nrog cov tsos mob hnyav thiab kub taub hau. Feem ntau, xws li pathology yog tsim los ntawm 3 xyoos thiab xaus los ntawm kev puberty.

menyuam thiab kws kho mob
menyuam thiab kws kho mob

chav kho mob

Nrog rau kev loj hlob ntawm lymphatic-hypoplastic diathesis hauv cov menyuam yaus, feem ntau tsis muaj qhov tshwj xeeb tshwj xeeb tshwm sim thiab kev tsis txaus siab. Txawm li cas los xij, kev kuaj mob qhia ntau yam kev mob tshwm sim thiab cov tsos mob pathological. Feem ntau, cov menyuam yaus no raug kev txom nyem los ntawm kev rog dhau, thiab qhov no pom tau los ntawm thawj hnub ntawm lub neej. Lawv muaj cov tawv nqaij daj ntseg, muag heev thiab tawm hws ntau dhau. Cov tawv nqaij ntawm ko taw thiab xib teg yog moist rau qhov kov.

Lymphatic-hypoplastic diathesis hauv cov menyuam yaus yog tus cwj pwm los ntawm lethargy thiab irritability, xws li cov menyuam yaus feem ntau tsis ua haujlwm thiab qaug zog. Lawv muaj kev qaug zog sai, kev lag luam hauv psychomotor kev loj hlob, thiab txo cov ntshav siab. Cov me nyuam zoo li no tsis zam qhov kev hloov ntawm ib puag ncig.ib puag ncig thiab tsev neeg tsis sib haum xeeb. Nws nyuaj rau lawv hloov mus rau cov xwm txheej tshiab.

Nrog exudative diathesis (daim duab hauv qab no), nquag ua xua ua pob liab vog tau pom, thaj chaw feem ntau ntawm pob tw thiab qis qis. Cov tawv nqaij folds tuaj yeem ua rau daim pawm ua pob khaus thiab marbling ntawm daim tawv nqaij.

Lawv muaj qhov nce ntxiv hauv txhua lub hauv nruab nrog cev uas muaj cov ntaub so ntswg lymphoid. Qhov no qhia tau tias yuav luag nce ntxiv:

  • lymph nodes;
  • tonsils thiab adenoids;
  • spleen (tej zaum yuav raug kuaj pom thaum lub sijhawm ultrasound).

Lub cev ntawm cov menyuam yaus raug kev txom nyem los ntawm qhov tsis txaus ntseeg: ntawm kev kuaj xyuas, cov ceg ntev ntev thiab kev faib tawm tsis sib xws ntawm cov roj subcutaneous (feem ntau nws nyob hauv lub cev hauv qab) tau tshwm sim.

pub mis rau menyuam
pub mis rau menyuam

Kev loj hlob ntawm tonsils thiab adenoids yuav tsum ceeb toom rau niam txiv thiab tus kws kho mob. Yog tias qhov ntsuas zoo sib xws nyob sab nraud ntawm qhov exacerbation, thaum lub sijhawm muaj mob lawv yuav loj dua. Hauv qhov no, hypertrophy ntawm adenoids thiab tonsils tuaj yeem thaiv kev nkag mus ntawm cov pa oxygen mus rau txoj hlab pa thiab cuam tshuam cov txheej txheem nqos. Tsis tas li ntawd, lawv qhov kev nce ntxiv feem ntau ua rau mob khaub thuas ntev nrog los ntawm qhov ntswg.

Hypertrophy ntawm tonsils thiab adenoids yuav tsum muaj kev phais mob, vim nws tuaj yeem ua rau cov pa oxygen tshaib plab ntawm cov kabmob thiab cov kab ke ntawm lub cev, nrog rau cuam tshuam rau lub xeev ntawm lub hlwb. Cov xwm txheej zoo li no ua rau muaj kev txhim khoKev tsis txaus siab ntawm kev mloog lus thiab kev nco tsis zoo, uas cuam tshuam rau kev ua haujlwm hauv tsev kawm ntawv. Sij hawm dhau mus, qhov tsis muaj oxygen pib cuam tshuam rau qhov tsos. Nrog lymphatic-hypoplastic diathesis hauv cov menyuam yaus (cov duab ntawm ntau qhov chaw kho mob ua pov thawj rau qhov no), cov kev hloov pauv tshwj xeeb tshwm sim hauv cov qauv ntawm lub cranium, xws li:

  • nce thiab lub puab tsaig sab sauv pib protrude;
  • qhov ncauj yuav luag ib nrab qhib;
  • ntsej muag daj;
  • puffiness tshwm.

Cov paib no maj mam tsim, tab sis yog tias lawv tshwm sim, lawv tseem nyob mus ib txhis. Nws tsis muaj peev xwm tshem tau lawv, txawm tias cov adenoids raug tshem tawm.

zoo siab tus me nyuam tsis muaj diathesis
zoo siab tus me nyuam tsis muaj diathesis

Lwm yam khoom

Cov menyuam yaus uas muaj kab mob no feem ntau muaj qee qhov sib txawv hauv kev loj hlob ntawm cov kabmob sab hauv. Feem ntau, qhov tsim ntawm lymphatic-hypoplastic diathesis yog tshwm sim hauv kev loj hlob ntawm lub plawv. Cov niam txiv ntawm cov menyuam yaus no yuav tsum txhawj xeeb txog qhov nquag pallor lossis xiav nasolabial daim duab peb sab thiab pw tsaug zog apnea, tshwj xeeb tshaj yog thaum pw tsaug zog.

Tsis tas li ntawd, lawv muaj ntau yam cim qhia ntawm dysembryogenesis: cov hlab ntsha loj, ob lub raum, cov kab mob hauv nruab nrog cev, cov qog endocrine, thiab tseem muaj cov kab mob me me. Qhov no tso cai rau peb los txhais qhov tshwm sim no li lymphatic-hypoplastic diathesis.

Diagnosis

Feem ntau, xws li pathology raug kuaj los ntawm cov ntaub ntawv tau txais tom qab kuaj thiab sau cov anamnesis ntawm tus neeg mob. Qhov no coj mus rau hauv tus account lub xeevlymph nodes tsis exacerbation ntawm tej kab mob thiab hypertrophy ntawm tonsils thiab adenoids.

lub hauv siab x-ray feem ntau qhia txog kev hloov pauv hauv lub caj pas thymus. Tsis tas li ntawd, nws muaj peev xwm txheeb xyuas cov kev hloov pauv hauv lub siab. Nrog lymphatic-hypoplastic diathesis nyob rau hauv cov me nyuam, thaum lub sij hawm ultrasound diagnostics, ib qho kev nce nyob rau hauv tus po yog pom nrog ib txwm daim siab loj.

Kev Tshawb Fawb Kev Tshawb Fawb

Thaum ua kev kuaj ntshav hauv cov menyuam yaus uas raug kev txom nyem los ntawm cov kab mob no, pom muaj cov tsos mob ntawm lymphocytosis kiag li thiab txheeb ze, neutro- thiab monocytopenia. Ntshav biochemistry qhia tau tias txo qis hauv cov ntshav qabzib, nrog rau kev nce hauv cov roj cholesterol thiab phospholipids.

Y Thaum ua cov tshuaj tiv thaiv kab mob, qhov txo qis hauv IgA, IgG, tus naj npawb ntawm T- thiab B-lymphocytes, ua txhaum ntawm qhov sib piv ntawm T-helpers / T-suppressors, thiab kev nce ntxiv ntawm kev tiv thaiv kab mob hauv lub cev. kuaj pom. Kev txo qis hauv qhov concentration ntawm thymus yam hauv cov ntshav thiab 17-ketosteroids hauv kev kuaj zis yog txiav txim siab.

tus menyuam tsis haum
tus menyuam tsis haum

Kev kho cov lymphatic-hypoplastic diathesis hauv cov menyuam yaus

Txog hnub no, tsis muaj kev kho tshwj xeeb rau tus mob pathological no. Qhov tseem ceeb heev rau kev ntxiv dag zog rau tus menyuam txoj kev tiv thaiv yog nquag taug kev thiab ua si hauv huab cua ntshiab, ua raws li kev ua haujlwm niaj hnub thiab ua kom muaj kev noj qab haus huv.

Cov kws kho mob feem ntau nrog lymphatic-hypoplastic diathesis pom zoo kom hloov pauv rau cov menyuam yaus (ginseng tincture, glycyram, licorice hauv paus, extractEleutherococcus), uas yuav tsum tau coj mus rau hauv cov chav kawm. Qee zaum, tus menyuam yuav raug muab tshuaj bificol, bifidumbacterin, thiab calcium ntxiv.

Cov txiaj ntsig zoo tuaj yeem tau txais los ntawm kev noj tshuaj "Lymphomiazot", uas pab ua kom lub cev ua haujlwm ntawm lymphatic. Qee zaum, nws muab txo qhov loj ntawm tonsils thiab adenoids.

Nrog rau kev loj hlob sai adenoid, cov tshuaj niaj hnub muab lawv tshem tawm los ntawm kev phais. Tau kawg, cov txheej txheem no tsuas yog ua tiav thaum tsis muaj qhov ntswg ua pa lossis nrog nquag rov ua dua ntawm cov kab mob ua pa ntawm cov pa.

Vim cov menyuam raug kev txom nyem los ntawm kev tsis haum tshuaj hnyav nrog cov xwm txheej zoo li no, nws yog ib qho tsim nyog yuav tsum tau noj zaub mov kom tiav thiab sib npaug. Kev siv cov khoom uas muaj hluavtaws dyes thiab preservatives yog tsis tsim nyog.

Nyob rau hauv cov xwm txheej zoo li no, kev kho tus kheej tsis tuaj yeem siv, vim tias tseem muaj kev pheej hmoo ua rau kev noj qab haus huv ntawm cov kab mob tsis muaj zog. Txhua yam kev kho mob yuav tsum tau muab los ntawm kws kho mob.

zaub hauv me nyuam noj
zaub hauv me nyuam noj

Txoj cai noj zaub mov thiab noj zaub mov

Cov zaub mov ntxiv yuav tsum tau nthuav tawm maj mam thiab ceev faj, saib xyuas qhov ua tsis txaus ntawm lub cev.

Kev saib xyuas tshwj xeeb hauv qhov no yuav tsum tau qhia cov mis nyuj thiab cov khoom siv mis nyuj. Cov zaub mov zoo li no yuav tsum tshwm sim hauv tus menyuam noj tsis pub dhau 8 lub hlis. Tsis tas li ntawd, nws yog ib qho tsim nyog los txwv kev noj cov khoom qab zib. Nyob rau tib lub sijhawm, cov menyuam yaus cov ntawv qhia zaub mov yuav tsum muaj cov txiv hmab txiv ntoo thiab zaub uas sib haumcaij nyoog thiab thaj chaw. Tag nrho cov khoom noj uas siv yuav tsum yog cov tsis ua xua.

ntxhais noj txiv apple
ntxhais noj txiv apple

Huab cua

Cov menyuam yaus uas muaj keeb kwm ntawm qhov tsis zoo no tsis tuaj yeem tiv taus ntau yam kab mob, yog li lawv feem ntau mob. Nyob rau tib lub sijhawm, daim duab kho mob ntawm cov kab mob hauv lawv tau hais ntau dua thiab nrog rau kev kawm hnyav. Hauv cov menyuam yaus thaum ntxov, cov menyuam yaus uas kuaj mob thymomegaly yuav tsum tau saib xyuas zoo vim tias muaj kev pheej hmoo ntawm kev ua tsis taus pa. Yog tias koj mob khaub thuas, mob qhov ntswg, snoring thaum pw lossis hmo ntuj apnea, koj yuav tsum sab laj nrog kws kho mob otolaryngologist.

Raws li kev txheeb cais, kev tuag ntawm cov menyuam mos uas tau kuaj pom "thymomegaly" yog kwv yees li 10%. Feem ntau, cov tsos mob ntawm tus kab mob no ploj mus thaum hluas thaum lub sij hawm puberty. Txawm li cas los xij, qee zaus, thymico-lymphatic xwm txheej yuav nyob twj ywm rau lub neej.

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